[Mucocutaneous lymph node syndrome or infantile perlarteritis nodosa with extensive vascular involvement].
The authors report on a male infant displaying all the clinical features of the mucocutaneous lymph node syndrome (MLNS) as described by Kawasaki in 1967. In the same patient, diffuse dilatation of the whole arterial tree--as known in infantile periarteriitis nodosa but so far not shown in MLNS--could be demonstrated angiographically during the acute phase of the disease. As the vascular findings at postmortem examination in MLNS and periarteriitis nodosa were the same too, the authors believe that separation of these diseases is not justified.
D000783:Aneurysm / Q000175:diagnosis; D001014:Aortic Aneurysm / Q000175:diagnosis; D003327:Coronary Disease / Q000209:etiology; D006801:Humans; D006978:Hypertension, Renovascular / Q000175:diagnosis; D007223:Infant; D007231:Infant, Newborn; D008206:Lymphatic Diseases / Q000175:diagnosis*; D008297:Male; D009080:Mucocutaneous Lymph Node Syndrome / Q000175:diagnosis*; D010488:Polyarteritis Nodosa; D013348:Subclavian Artery
Mucocutanes Lymphknoten-Syndrom oder Infantile Periarteritiitis nodosa mit ausgedehnter Gefässbeteiligung.