[Pseudo-Hirschsprung's disease (author's transl)].
Eight children with pseudo-Hirschsprung's disease are reported. They can be divided into three groups: alimentary ganglioneuromatosis, schwann cell hyperplasia and those with normal appearance by stantard histology. In view of the heterogeneity, histology cannot predict the extent or the prognosis of the disease. Several biopsies at various levels of the alimentary tract and the use of advanced techniques are necessary to assess fully the extent and the type of the lesion and whether it is congenital or acquired. The majority of pseudo-Hirschsprung's disease tend to affect most of alimentary tract, which may lead to the formation of stagnant loops with all their risks. Treatment includes ileostomy, continuous hypoallergenic oral feeding, and manual expression several times a day.
D002648:Child; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D006965:Hyperplasia; D007223:Infant; D007231:Infant, Newborn; D007422:Intestines / Q000473:pathology; D008297:Male; D008531:Megacolon / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology / Q000628:therapy; D009197:Myenteric Plexus / Q000473:pathology; D018377:Neurotransmitter Agents / Q000032:analysis; D011859:Radiography
D018377:Neurotransmitter Agents
Démembrement du cadre "pseudo-Hirschsprung". A propos de 8 observations pédiatriques.