title: [Hereditary pancreatitis in early childhood (author's transl)].
abstract: Hereditary pancreatitis was diagnosed in dystrophic boy at the age of 2 1/2 years after recurring episodes of severe abdominal pain. Extensive left-sided pleural effusions caused surgical exploration. Pancreatography showed typical dilation of the pancreatic ductal system. After hemipancreatectomy by the boy recovered very fast. Characteristic features in diagnosing of hereditary pancreatitis are the onset of recurring attacks of abdominal pain in early childhood and anatomical defects in the pancreatic ductal system. The disease shows variability between family members.
mesh_terms: D002675:Child, Preschool; D006801:Humans; D008297:Male; D010180:Pancreatectomy; D010183:Pancreatic Ducts / Q000000981:diagnostic imaging; D010195:Pancreatitis / Q000150:complications / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D010996:Pleural Effusion / Q000150:complications; D011859:Radiography
vernacular_title: Hereditäre Pankreatitis im Kleinkindesalter.