Increased non-protein-bound iron and decreased protection against superoxide-radical damage in cerebrospinal fluid from patients with neuronal ceroid lipofuscinoses.
D000293:Adolescent; D000367:Age Factors; D002493:Central Nervous System Diseases / Q000134:cerebrospinal fluid*; D002566:Ceroid / Q000378:metabolism; D002648:Child; D002675:Child, Preschool; D005609:Free Radicals; D006801:Humans; D007223:Infant; D007501:Iron / Q000134:cerebrospinal fluid*; D008062:Lipofuscin / Q000378:metabolism*; D009474:Neurons; D010084:Oxidation-Reduction; D010860:Pigments, Biological / Q000378:metabolism*; D011485:Protein Binding; D013106:Sphingolipidoses / Q000134:cerebrospinal fluid*; D013481:Superoxides / Q000134:cerebrospinal fluid
D002566:Ceroid; D005609:Free Radicals; D008062:Lipofuscin; D010860:Pigments, Biological; D013481:Superoxides; D007501:Iron