Hairy cell leukemia and a fatal periarteritis nodosa-like syndrome.
We studied a patient with hairy cell leukemia (HCL) in whom periarteritislike lesions of multiple medium-sized arteries developed. There were many aneurysms distributed through the visceral organs. One ruptured into the abdomen, causing death. A previous study suggested that HCL may predispose to periarteritis nodosa, but recently a reversed temporal sequence of vasculitis and HCL was postulated. Our patient's course lends further support to the concept that HCL predisposes to vasculitis and periarteritislike lesions.
D000328:Adult; D000783:Aneurysm / Q000150:complications / Q000473:pathology; D002445:Celiac Artery / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006499:Hepatic Artery / Q000473:pathology; D006801:Humans; D007943:Leukemia, Hairy Cell / Q000150:complications / Q000473:pathology*; D010488:Polyarteritis Nodosa / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D013154:Spleen / Q000473:pathology; D013577:Syndrome