3-methyl-3-butenoic acid: an artefact in the urinary metabolic pattern of patients with 3-hydroxy-3-methylglutaryl-CoA lyase deficiency.
D000214:Acyl Coenzyme A / Q000172:deficiency; D000592:Amino Acid Metabolism, Inborn Errors / Q000652:urine*; D002087:Butyrates / Q000652:urine*; D003437:Crotonates / Q000652:urine*; D006801:Humans; D015093:Meglutol / Q000031:analogs & derivatives / Q000172:deficiency; D007652:Oxo-Acid-Lyases / Q000172:deficiency*
D000214:Acyl Coenzyme A; D002087:Butyrates; D003437:Crotonates; C011546:senecioic acid; D015093:Meglutol; D007652:Oxo-Acid-Lyases; C021410:3-hydroxy-3-methylglutaryl-coenzyme A lyase