Hyperamylasemia, duodenal duplication, and pleural effusions in hereditary spherocytosis.
A 15-year-old girl with hereditary spherocytosis was admitted for evaluation of recurrent pleural effusions containing amylase in high concentration and was found to have biliary obstruction, pancreatitis, and a congenital duplication of the duodenum attached to an accessory lobe of the pancreas via the duct of Santorini, a unique entity. Successful surgical management of these disorders included common duct clearance and anastomosis of the duplication to the adjacent duodenum.
D000293:Adolescent; D000681:Amylases / Q000097:blood; D004386:Duodenum / Q000002:abnormalities* / Q000601:surgery; D005260:Female; D006801:Humans; D010195:Pancreatitis / Q000175:diagnosis / Q000209:etiology*; D010996:Pleural Effusion / Q000209:etiology*; D013103:Spherocytosis, Hereditary / Q000150:complications* / Q000175:diagnosis
D000681:Amylases