Inducible polymorphous ventricular tachycardia following Mustard operation for transposition of the great arteries.
A 22-year-old woman with chronic atrial tachycardia following Mustard's operation for transposition of the great arteries presented with dizziness and ventricular tachycardia documented with dynamic 24-h electrocardiogram. During intracardiac electrophysiology study, programmed ventricular extrastimulation induced polymorphous ventricular tachycardia (torsades de pointes). This was prevented by intravenous administration of procainamide. We postulate that polymorphous ventricular tachycardia is a possible cause of death in patients with Mustard's operation. Postoperative electrophysiologic study may define those patients at risk to develop this potentially fatal arrhythmia.
D000328:Adult; D005117:Cardiac Complexes, Premature / Q000209:etiology; D005080:Exercise Test; D005260:Female; D006327:Heart Block / Q000209:etiology; D006801:Humans; D011183:Postoperative Complications / Q000209:etiology*; D011342:Procainamide / Q000627:therapeutic use; D013575:Syncope / Q000209:etiology; D013610:Tachycardia / Q000188:drug therapy / Q000209:etiology*; D014188:Transposition of Great Vessels / Q000601:surgery*
D011342:Procainamide