Pulmonary valvulotomy in Factor XI deficiency.
This is the first reported case in the English literature of Factor XI deficiency in a child from India. He underwent open-heart surgery and pulmonary valvulotomy without excessive or delayed hemorrhage using plasma infusion to sustain Factor XI levels at about 40% of normal before, and for 10 days after surgery. The management of this child is presented as an approach to patients with Factor XI deficiency who require major surgery.
D002675:Child, Preschool; D005173:Factor XI Deficiency / Q000150:complications*; D006801:Humans; D008297:Male; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000601:surgery*