[Rigid spine syndrome and its nosological borders. 2 cases].
The rigid spine syndrome is characterized clinically by rigidity due to deficient extensor muscles of the spine (chiefly cervical) and radiologically, by a normal spinal image. Electromyography demonstrates abnormalities suggestive of a myogenic process, and histology shows alterations of muscular fibres. From the case-records of two male patients aged 14 and 15 years respectively, a relationship could be established between various diseases having in common a rigid spine syndrome. These include congenital muscular dystrophias , sequelae of arthrogryposis, Emery - Dreifuss myopathy and myosclerosis .
D000293:Adolescent; D006801:Humans; D008297:Male; D009127:Muscle Rigidity / Q000145:classification / Q000150:complications* / Q000473:pathology; D009136:Muscular Dystrophies / Q000145:classification; D013122:Spinal Diseases / Q000145:classification / Q000175:diagnosis*; D013577:Syndrome
Le syndrome de la colonne vertébrale rigide et ses frontières nosologiques. Deux observations.