Histopathological and ultrastructural findings in a case of Papillon-Lefèvre syndrome.
Gingiva from a 3-year-old Iranian boy suffering from Papillon-Lefèvre syndrome was examined by light and electron microscopy. Deep pockets associated with predominantly Gram-negative plaque were present. The gingival lesion was dominated by plasma cells, many of which were degenerate. Russell bodies were a prominent feature. No defect of epithelium was detected.
D002675:Child, Preschool; D005881:Gingiva / Q000648:ultrastructure; D005882:Gingival Diseases / Q000473:pathology*; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000473:pathology*; D007962:Leukocytes / Q000648:ultrastructure; D008297:Male; D008854:Microscopy, Electron; D010214:Papillon-Lefevre Disease / Q000473:pathology*; D010950:Plasma Cells / Q000648:ultrastructure