Plain radiographic, nuclear medicine and angiographic observations of hepatogenic pulmonary angiodysplasia.
Clinical and radiological findings of hepatogenic pulmonary angiodysplasia are reported in two cases. Myriad spidery pulmonary blood vessels are seen on plain radiographs and verified with right to left intrapulmonary shunting on pulmonary angiogram and pulmonary isotopic perfusion scan. Pathophysiology and differential diagnosis are discussed. We propose that the term "pulmonary angio-dysplasia" should include: 1) Pulmonary telangiectasia 2) Hereditary hemorrhagic telangiectasia (Osler-Rendu-Weber syndrome) 3) Classical discrete pulmonary arteriovenous fistula 4) Hepatogenic pulmonary angiodysplasia: pulmonary arteriovenous communications with right to left shunting secondary to hepatic cirrhosis.
D000293:Adolescent; D000792:Angiography; D001165:Arteriovenous Malformations / Q000175:diagnosis*; D002648:Child; D006801:Humans; D008103:Liver Cirrhosis / Q000150:complications*; D008168:Lung / Q000098:blood supply / Q000000981:diagnostic imaging; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities*; D011667:Pulmonary Veins / Q000002:abnormalities*; D011877:Radionuclide Imaging; D012709:Serum Albumin; D013667:Technetium; D013668:Technetium Tc 99m Aggregated Albumin; D013684:Telangiectasis / Q000175:diagnosis*
D012709:Serum Albumin; D013668:Technetium Tc 99m Aggregated Albumin; D013667:Technetium