[Angiomatous dysplasia (Weber type) (author's transl)].
A rare form of angiomatous dysplasia with hypotrophy of the left arm is described. Numerous haemodynamically significant arterio-venous fistulae could be demonstrated in the soft tissues and in bone. The venous and lymphatic systems were normal. The lacunar reticular-cystic changes in the spongiosa of the phalanges are pathognomonic of arterial angiodysplasia of the Weber type. In most cases this is associated with bone hypertrophy.
D000293:Adolescent; D000792:Angiography; D000798:Angiomatosis / Q000000981:diagnostic imaging*; D001132:Arm / Q000098:blood supply; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D013341:Sturge-Weber Syndrome / Q000000981:diagnostic imaging*
Angiomatöse Dysplasie (Typ F.P. Weber).