[Adult Still's disease with constrictive pericarditis, Sjögren's syndrome and varied leucocytic abnormalities (author's transl)].
Adult Still's disease is a newly described disorder that is of interest not only for the rheumatologist but also for the internist since fever or extra-articular symptoms can reveal this disorder, which appears to be identical to the Wissler-Fanconi's syndrome. We report a new case characterized by the occurrence of a constrictive pericarditis with clinical features of protracted fever, by the late appearance of a Sjögren's syndrome and by peculiar blood abnormalities: hyperleucocytosis up to 80 000 after splenectomy, transient Felty's syndrome, blood monocytosis and bone marrow mastocytosis.
D001171:Arthritis, Juvenile / Q000150:complications*; D002908:Chronic Disease; D005260:Female; D006801:Humans; D007962:Leukocytes / Q000473:pathology*; D008875:Middle Aged; D010493:Pericarditis / Q000150:complications*; D012859:Sjogren's Syndrome / Q000150:complications*
Maladie de Still de l'adulte avec péricaedite chronique, syndrome SEC et anomalies leucocytaires diverses.