title: [Cholangio-carcinoma arising in Caroli's disease (author's transl)].
abstract: Report of one case of Caroli's disease (congenital ectasy of segmental intra-hepatic bile ducts) associated with congenital hepatic fibrosis, in which arised clear cell biliary carcinoma. This event seems to be very rare. In our case, the bile duct dilatation was associated with renal polycystic diseases.
mesh_terms: D000230:Adenocarcinoma / Q000150:complications*; D000328:Adult; D001649:Bile Duct Diseases / Q000150:complications / Q000151:congenital; D001650:Bile Duct Neoplasms / Q000150:complications*; D001653:Bile Ducts, Intrahepatic / Q000473:pathology*; D003560:Cysts / Q000150:complications; D004108:Dilatation, Pathologic; D006801:Humans; D008297:Male; D007690:Polycystic Kidney Diseases / Q000150:complications
vernacular_title: Carcinomie biliaire développé sur maladie de Caroli. A propos d'un cas.