[Chronic hepatopathy and progressive systemic sclerosis. Frequency of association with Gougerot-Sjögren's disease. A report on six new cases (author's transl)].
Six patients with scleroderma (Barnett's type I and II) associated with hepatopathy are reported. Primary biliary cirrhosis was confirmed in four cases and was probably present in one case, while cirrhosis of unknown origin was present in the sixth patient. The outcome was fatal in two cases. Salivary secretions were reduced in all six cases, and a diagnosis of Gougerot-Sjögren's disease was confirmed in four patients. The frequency with which this triple association has been reported suggests that its incidence has been underestimated.
D000328:Adult; D005260:Female; D006505:Hepatitis / Q000150:complications; D006801:Humans; D008103:Liver Cirrhosis / Q000150:complications; D008105:Liver Cirrhosis, Biliary / Q000150:complications; D008107:Liver Diseases / Q000150:complications* / Q000276:immunology; D008875:Middle Aged; D012595:Scleroderma, Systemic / Q000150:complications*; D012859:Sjogren's Syndrome / Q000150:complications*
Hépatopathies chroniques et sclérodermie systémique. Fréquence de l'association avec un syndrome de Gougerot-Sjögren. A propos de six nouvelles observations.