Neoplasms associated with hemihypertophy, Beckwith-Wiedemann syndrome and aniridia.
Hemihypertophy and the Beckwith-Wiedemann syndrome are associated with Wilms tumor and adrenocortical carcinoma. These conditions also have a relationship with nodular renal blastema, nephroblastomatosis and adrenocortical adenomas, all of which are pre-malignant lesions. children with aniridia also are predisposed to development of Wilms tumors.
D000015:Abnormalities, Multiple / Q000235:genetics*; D000306:Adrenal Cortex Neoplasms / Q000150:complications*; D002675:Child, Preschool; D005260:Female; D005317:Fetal Growth Retardation / Q000150:complications; D006801:Humans; D006984:Hypertrophy / Q000150:complications; D007498:Iris / Q000002:abnormalities*; D007680:Kidney Neoplasms / Q000150:complications* / Q000235:genetics; D008297:Male; D011247:Pregnancy; D014059:Tongue / Q000002:abnormalities; D009396:Wilms Tumor / Q000150:complications* / Q000235:genetics