[Therapeutic indications in scoliosis of Duchenne muscular dystrophy. Apropos of 10 cases].
Ten patients suffering from Duchenne muscular dystrophy were followed up for more than 7 years. The diagnosis was determined by biopsy. Progress of the disease was severe and all patients died before the age of 18. The average angle of the scoliosis at the end of this development was 73 degrees. The maximum vital capacity was 1198 ml. The authors conclude that neither the use of a brace nor adaptation of a wheelchair are helpful. Surgical treatment is hazardous when the curve is greater than 23 degrees. The indications for such treatment are based on the importance of the degree of pulmonary restriction and on early signs of severe progress of the scoliosis.
D002675:Child, Preschool; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D009136:Muscular Dystrophies / Q000150:complications*; D012600:Scoliosis / Q000209:etiology / Q000601:surgery / Q000628:therapy*; D013997:Time Factors
Indications thérapeutiques dans la scoliose de la dystrophie musculaire de Duchenne. A propos de 10 cas.