[Haemoperitoneum due to ruptured hepatoma in a cirrhotic patient with porphyria cutanea tarda. Three years' survival (author's transl)].
A case of ruptured hepatocarcinoma of the left lobe in a cirrhotic patient with a 7 years' history of porphyria cutanea tarda (PCT) is reported. Emergency left lobectomy resulted in 3 years' survival with no sign of recurrence at present. Comments are made concerning the clinical association PCT-hepatoma: (1) either PCT is associated with a hypersecretory hepatoma and behaves as a neoplastic syndrome following the same course as the tumour; (2) or PCT is associated with a cirrhosis (usually alcoholic) which facilitates the development of a hepatoma. In such cases, PCT precedes the tumour and follows a separate course.
D000368:Aged; D006528:Carcinoma, Hepatocellular / Q000150:complications* / Q000601:surgery; D006465:Hemoperitoneum / Q000209:etiology*; D006498:Hepatectomy; D006801:Humans; D008104:Liver Cirrhosis, Alcoholic / Q000150:complications*; D008113:Liver Neoplasms / Q000150:complications* / Q000601:surgery; D008297:Male; D011164:Porphyrias / Q000150:complications; D012422:Rupture, Spontaneous; D012871:Skin Diseases / Q000150:complications
Hémopéritoine par rupture d'un hépatome chez un cirrhotique atteint de porphyrie cutanée tardive. Survie de 3 ans après hépatectomie.