["Deep scleroderma" or diffuse fibromatous scleroderma. A case-report of uncertain nosologic classification (author's transl)].
An unusual form of scleroderma, seen in one patient, is described. Clinical and histological examinations demonstrated no dermal changes. Both the subcutaneous tissue and the fascias were involved. This case can be distinguished from Shulman fasciitis, on both histological and biological grounds, as well as from scleroderma, since Raynaud phenomena, sclerodactylia, and visceral involvement were lacking.
D000328:Adult; D003937:Diagnosis, Differential; D004802:Eosinophilia / Q000473:pathology; D005205:Fascia / Q000473:pathology; D005208:Fasciitis / Q000473:pathology; D005350:Fibroma / Q000473:pathology; D006801:Humans; D008297:Male; D012595:Scleroderma, Systemic / Q000175:diagnosis / Q000473:pathology*; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000473:pathology
"Sclérodermie profonde" ou fibromatose diffuse. A propos d'un cas de nosologie incertaine.