[Malignant systemic mastocytosis (author's transl)].
The case of a 37 year old man with systemic malignant cutaneous mastocytosis is reported. The outcome was fatal after eight months. Death was due to a diffuse hemorrhagic syndrome which originated in an abnormal circulating heparinoid. Nosologically, this is a border-line case between mast cell leukemia and leukemic systemic mastocytosis.
D000328:Adult; D001778:Blood Coagulation Disorders / Q000209:etiology; D006801:Humans; D008297:Male; D012867:Skin / Q000473:pathology; D013156:Splenectomy; D014582:Urticaria Pigmentosa / Q000150:complications / Q000175:diagnosis* / Q000473:pathology
Mastocytose systémique maligne.