title: [Auricular arrhythmia in Steinert's myotonia. Apropos of a case with a familial study].
abstract: A case of bradycardia-tachycardia syndrome leading to the late discovery of Steinert syndrome is reported. There is a discrepancy between the frequency of the main features of the bradycardia-tachycardia syndrome (sinoatrial block and atrial flutter in our observation) usually reported in Steinert disease and the fact that no case similar to ours seems to have yet been reported; this suggests definite underrating. Insertion of a pacemaker should avoid sudden death from a conduction disturbance. The heart should be carefully monitored in patients with myotonic dystrophy; conversely, this diagnosis should be considered in the etiologic diagnosis of myocardiopathies.
mesh_terms: D001145:Arrhythmias, Cardiac / Q000209:etiology* / Q000628:therapy; D001282:Atrial Flutter / Q000209:etiology; D001919:Bradycardia / Q000209:etiology; D004562:Electrocardiography; D005260:Female; D006325:Heart Atria / Q000503:physiopathology; D006801:Humans; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000175:diagnosis* / Q000235:genetics; D010138:Pacemaker, Artificial; D012848:Sinoatrial Block / Q000209:etiology
vernacular_title: Maladie rythmique auriculaire au cours d'une myotonie de Steinert. A propos d'un cas avec enquête familiale.