title: [Excitatory conduction in motor fibers of peripheral nerves in hereditary-degenerative diseases in children].
abstract: The authors carried out clinico-morphological and electrophysiological comparisons in such pronounced forms of pathology, as ceroid lipofuscinosis, metachromatic leukodystrophy, subacute necrotizing encephalomyelitis. The determination of the speed of stimulus conduction along the efferent nerves is a method of early diagnosis of metachromatic leukodystrophy. This method also facilitates the estimation of the pathological process gravity in other diseases.
mesh_terms: D002675:Child, Preschool; D004679:Encephalomyelitis / Q000201:enzymology / Q000503:physiopathology; D006801:Humans; D007223:Infant; D007966:Leukodystrophy, Metachromatic / Q000473:pathology / Q000503:physiopathology; D009046:Motor Neurons / Q000502:physiology*; D009431:Neural Conduction; D009472:Neuronal Ceroid-Lipofuscinoses / Q000473:pathology / Q000503:physiopathology*; D010525:Peripheral Nerves / Q000503:physiopathology* / Q000648:ultrastructure; D010770:Phosphotransferases / Q000378:metabolism; D017856:Phosphotransferases (Phosphate Group Acceptor)
chemical_list: D010770:Phosphotransferases; D017856:Phosphotransferases (Phosphate Group Acceptor); C022733:thiamin-diphosphate kinase
vernacular_title: Provodimost' vozbuzhdeniia v dvigatel'nykh voloknakh perifericheskikh nervov pri nasledstvenno-degenerativnykh zabolevaniiakh u deteĭ.