[Results of the surgical treatment of fibrocholangiocystosis of the liver in children].
A rare hereditary disease of the liver (fibrocholangiocystosis--congenital fibrosis of the liver) was surgically treated in 43 children. A conclusion is made that different palliative operations are inexpedient. Ilio-cavamesenterial anastomoses may be recommended for preventing relapses of gastroesophageal hemorrhages. These operations should be performed at the age of 5-10 years. After palliative operations recurrent hemorrhages were noted in 68,4%, lethality in 26,3%. After vascular anastomoses recurrent hemorrhages were found in 23,3%, lethality--in 7,7%.
D000293:Adolescent; D001649:Bile Duct Diseases / Q000150:complications / Q000601:surgery*; D001653:Bile Ducts, Intrahepatic / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D004932:Esophageal and Gastric Varices / Q000150:complications / Q000601:surgery; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000150:complications / Q000601:surgery; D006801:Humans; D006975:Hypertension, Portal / Q000517:prevention & control; D007223:Infant; D008105:Liver Cirrhosis, Biliary / Q000150:complications / Q000601:surgery*; D008297:Male; D011167:Portacaval Shunt, Surgical
Rezul'taty khirurgicheskogo lecheniia fibrokholangiokistoza pecheni u deteĭ.