Bullous amyloidosis associated with Bence Jones proteinemia without proteinuria.
A 74 yo female was found to have bullous dermal amyloidosis on the background of systemic amyloidosis with multiple myeloma. There was monoclonal immunoglobulin light chain of kappa type in the serum with no proteinuria (Bence Jones proteinemia without Bence Jones proteinuria), along with proliferations of kappa-producing plasma cells in the marrow.
D000368:Aged; D000686:Amyloidosis / Q000209:etiology* / Q000473:pathology; D001536:Bence Jones Protein / Q000097:blood / Q000652:urine; D001797:Blood Protein Electrophoresis; D005260:Female; D006801:Humans; D009101:Multiple Myeloma / Q000150:complications*; D012867:Skin / Q000473:pathology; D012872:Skin Diseases, Vesiculobullous / Q000209:etiology* / Q000473:pathology
D001536:Bence Jones Protein