[Aggressive therapy in a case of Moschowitz syndrome].
We report a case of thrombotic thrombocytopenic purpura which responded spectacularly to therapy consisting of corticosteroids, prostacyclin, high doses of platelet anti-aggregants and repeated plasma exchange. There was no anomaly of the von Willebrand factor VIII. The number of schizocytes and the lactate dehydrogenase level are as important as the beta-thromboglobulin dosage.
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use*; D001241:Aspirin / Q000627:therapeutic use*; D004176:Dipyridamole / Q000627:therapeutic use*; D004359:Drug Therapy, Combination; D011464:Epoprostenol / Q000627:therapeutic use*; D005260:Female; D006801:Humans; D008875:Middle Aged; D010951:Plasma Exchange; D011697:Purpura, Thrombotic Thrombocytopenic / Q000188:drug therapy* / Q000628:therapy
D000305:Adrenal Cortex Hormones; D004176:Dipyridamole; D011464:Epoprostenol; D001241:Aspirin
Aggressivité thérapeutique en cas de syndrome de Moschowitz.