Diet and growth of children with glycogen storage disease Types I and III.
Patients with glycogen storage disease (GSD) Types I and III were placed on a dietary treatment plan of frequent daytime feedings and continuous drip nocturnal enteral feedings of defined nutrient composition. Specific anthropometric measurements were collected to document and evaluate growth. There were a significant increase in arm muscle area and a relative decrease in triceps skinfold thickness not previously documented in the literature. Study results confirmed previous reports of accelerated growth and improvement of biochemical abnormalities. The dietitian's role in nutrition assessment and dietary management of GSD patients is emphasized.
D000293:Adolescent; D000328:Adult; D000886:Anthropometry; D001827:Body Height; D001835:Body Weight; D002648:Child; D002675:Child, Preschool; D004040:Dietary Carbohydrates / Q000008:administration & dosage; D004041:Dietary Fats / Q000008:administration & dosage; D004044:Dietary Proteins / Q000008:administration & dosage; D002149:Energy Intake; D004750:Enteral Nutrition; D006008:Glycogen Storage Disease / Q000628:therapy*; D005953:Glycogen Storage Disease Type I / Q000178:diet therapy / Q000378:metabolism / Q000628:therapy*; D006010:Glycogen Storage Disease Type III / Q000178:diet therapy / Q000378:metabolism / Q000628:therapy*; D006128:Growth; D006801:Humans; D007223:Infant; D009551:Night Care; D012885:Skinfold Thickness
D004040:Dietary Carbohydrates; D004041:Dietary Fats; D004044:Dietary Proteins