Anaesthesia and the mucopolysaccharidoses: a survey of techniques and problems.
Mucopolysaccharide infiltration of tissues in Hurler, Hunter, San Filippo, Maroteaux-Lamy, Morquio and Scheie syndromes causes problems to anaesthetists in the management of the airway and in myocardial function. Recent experience at the Royal Children's Hospital, Melbourne, is presented with illustrations highlighting these problems.
D000293:Adolescent; D000402:Airway Obstruction / Q000209:etiology; D000770:Anesthesia, Endotracheal / Q000379:methods*; D002648:Child; D002675:Child, Preschool; D003327:Coronary Disease / Q000150:complications; D006801:Humans; D007442:Intubation, Intratracheal / Q000379:methods*; D007830:Larynx / Q000002:abnormalities*; D009083:Mucopolysaccharidoses / Q000150:complications*; D009960:Oropharynx / Q000002:abnormalities*; D013514:Surgical Procedures, Operative