[The pathology of factor VIII in von Recklinghausen's disease: a new association].
A Von Willebrand's disease associated to Von Recklinghausen's disease is described. A an common alteration in the mesenchima is suggested as pathogenic mechanism. DDAVP was used as supportive treatment for bleeding, in preparation for surgery.
D001808:Blood Vessels / Q000196:embryology; D002648:Child; D004727:Endothelium / Q000196:embryology; D005260:Female; D006801:Humans; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000196:embryology; D012878:Skin Neoplasms / Q000150:complications* / Q000196:embryology; D013285:Strabismus / Q000150:complications; D014842:von Willebrand Diseases / Q000150:complications* / Q000196:embryology
Patología del factor VIII en la enfermedad de Recklinghausen: una nueva asociación.