Papillon-Lefèvre syndrome: a case report.
A case of Papillon-Lefèvre syndrome is presented. Hyperkeratosis of the palms and soles along with precocious destruction of the periodontal support of both the primary and permanent dentitions were observed. Ectopic intra-cranial calcified deposits, seen in some cases of the syndrome, were absent in this case. A greater awareness of this condition among dentists and dermatologists would be helpful in identifying more cases for study.
D000293:Adolescent; D000539:Alveolar Process; D001862:Bone Resorption / Q000473:pathology; D005881:Gingiva / Q000473:pathology; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000175:diagnosis*; D008297:Male; D010214:Papillon-Lefevre Disease / Q000175:diagnosis* / Q000209:etiology / Q000473:pathology; D010510:Periodontal Diseases / Q000473:pathology; D012867:Skin / Q000473:pathology