Systemic mastocytosis with diffuse crocodile-like pachydermic skin, pedunculated pseudofibromas and comedones.
A case of systemic mastocytosis is described, characterized by the severity of its cutaneous manifestations (diffuse encephaloid pachydermia, numerous skin tumours reminiscent of molluscum fibrosum, and large comedones) associated with gastro-intestinal disturbances and high blood histamine values but running a benign clinical course.
D000152:Acne Vulgaris / Q000209:etiology; D005260:Female; D005350:Fibroma / Q000209:etiology / Q000473:pathology; D006632:Histamine / Q000097:blood; D006801:Humans; D008875:Middle Aged; D012867:Skin / Q000648:ultrastructure; D012878:Skin Neoplasms / Q000209:etiology / Q000473:pathology; D014582:Urticaria Pigmentosa / Q000097:blood / Q000150:complications / Q000473:pathology*
D006632:Histamine