A case of the Kugelberg-Welander syndrome complicated with cardiac lesions.
There have been a few reports of cardiac involvement in the Kugelberg-Welander syndrome. We presented a case of this syndrome complicated with cardiomegaly and conduction disturbance. The patient, a 21-year-old woman, had atrial standstill and A-V junctional rhythm. The chest X-ray film showed marked cardiomegaly. The His bundle electrogram revealed that H-V interval was 40 msec. She was treated with implantation of cardiac pacemaker.
D000328:Adult; D001145:Arrhythmias, Cardiac / Q000175:diagnosis / Q000209:etiology*; D002304:Cardiac Pacing, Artificial; D006332:Cardiomegaly / Q000175:diagnosis / Q000209:etiology*; D004562:Electrocardiography; D005260:Female; D006329:Heart Conduction System / Q000503:physiopathology; D006801:Humans; D009133:Muscular Atrophy / Q000150:complications* / Q000235:genetics; D009206:Myocardium / Q000473:pathology