The pathophysiology of neurofibromatosis. II. Angiosarcoma as a complication.
A patient with Von Recklinghausen neurofibromatosis and an angiosarcoma (which developed subsequent to two separate neurofibrosarcomas ) is described, and the association of neurofibromatosis and angiosarcoma is reviewed. The data showed that angiosarcoma is not coincidental with neurofibromatosis, and there is a need to focus investigative efforts on the vascular aspects of this disease.
D000328:Adult; D006394:Hemangiosarcoma / Q000150:complications* / Q000473:pathology; D006801:Humans; D008175:Lung Neoplasms / Q000150:complications* / Q000473:pathology; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000473:pathology