Abdominal and extra-abdominal desmoid tumors. Report of 21 cases.
Desmoid tumors are easily diagnosed when located within the muscles of the abdominal wall. On the contrary, extra-abdominal desmoids, because of their various sites and lack of pathognomonic signs, can be very difficult to diagnose. A review of 21 cases of the Istituto Nazionale Tumori of Milan confirms that these tumors primarily affect young, multiparous women and that even extra-abdominal desmoids are prevalent in women. All patients were treated by radical surgery consisting of wide exicision in 18 cases, hemimandibulectomy in 1 case, and amputation of the lower limb in 2 cases. Radical surgery resulted in no recurrences in all cases but one. Our results are in contrast with the relatively high recurrence rates reported in the literature.
D000009:Abdominal Muscles; D000008:Abdominal Neoplasms / Q000601:surgery*; D000293:Adolescent; D000328:Adult; D000368:Aged; D002675:Child, Preschool; D005260:Female; D005350:Fibroma / Q000601:surgery*; D006801:Humans; D007866:Leg; D008297:Male; D008339:Mandibular Neoplasms / Q000601:surgery; D008875:Middle Aged; D009135:Muscular Diseases / Q000601:surgery; D009364:Neoplasm Recurrence, Local; D010298:Parity; D012737:Sex Factors