title: [Extrapalmoplantar skin symptoms and additional clinical, etiological and immunological aspects in particular, in Papillon-Lefevre syndrome].
abstract: Numerous patients with Papillon-Lefèvre syndrome show scaly erythematous lesions over knees, elbows and the interphalangeal joints additionally to the well known palmo-plantar hyperkeratosis. Not rarely, these skin symptoms are misdiagnosed as psoriasis. The obligatory and highly specific periodontitis marginalis profunda should lead to the correct diagnosis. A basic immune defect, which was shown in such a patient recently, could not be verified in the patient described here.
mesh_terms: D002648:Child; D003937:Diagnosis, Differential; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000473:pathology*; D008297:Male; D010214:Papillon-Lefevre Disease / Q000209:etiology / Q000276:immunology / Q000473:pathology*; D010518:Periodontitis / Q000209:etiology / Q000473:pathology
vernacular_title: Extrapalmoplantare Hautsymptome und weitere klinische und ätiologische, insbesondere immunologische Gesichtspunkte beim Papillon-Lefèvre-Syndrom.