Audiologic manifestations in bilateral acoustic tumors (von Recklinghausen's disease).
This report provides a review and discussion of bilateral acoustic tumors (von Recklinghausen's Disease) with emphasis on the audiological manifestations. To aid in our clinical description of this disease a series of 22 patients are summarized and three case reports are presented. The audiometric findings are shown to be quite different from what is generally seen in unilateral tumors. Because of the significant complications that can be associated with this disorder, especially in the later stages, the importance of early detection is emphasized. Strategies for audiologic management are also presented.
D000293:Adolescent; D000328:Adult; D002648:Child; D003638:Deafness / Q000209:etiology / Q000534:rehabilitation; D005260:Female; D005817:Genetic Counseling; D006319:Hearing Loss, Sensorineural / Q000209:etiology* / Q000534:rehabilitation; D006801:Humans; D008297:Male; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000473:pathology; D009464:Neuroma, Acoustic / Q000150:complications* / Q000473:pathology; D012050:Rehabilitation, Vocational; D000159:Vestibulocochlear Nerve / Q000473:pathology