Enzymatic phosphorylation of lysosomal enzymes in the presence of UDP-N-acetylglucosamine. Absence of the activity in I-cell fibroblasts.
D000818:Animals; D002478:Cells, Cultured; D005260:Female; D005347:Fibroblasts / Q000201:enzymology*; D006596:Hexosaminidases / Q000378:metabolism; D006801:Humans; D008247:Lysosomes / Q000201:enzymology*; D008360:Mannosephosphates / Q000096:biosynthesis; D008862:Microsomes, Liver / Q000201:enzymology; D009081:Mucolipidoses / Q000201:enzymology*; D010766:Phosphorylation; D010920:Placenta / Q000201:enzymology; D011247:Pregnancy; D051381:Rats; D012867:Skin; D014537:Uridine Diphosphate N-Acetylglucosamine / Q000378:metabolism*; D014539:Uridine Diphosphate Sugars / Q000378:metabolism*; D001619:beta-N-Acetylhexosaminidases
D008360:Mannosephosphates; D014539:Uridine Diphosphate Sugars; C027693:mannose-6-phosphate; D014537:Uridine Diphosphate N-Acetylglucosamine; D006596:Hexosaminidases; D001619:beta-N-Acetylhexosaminidases