Scintigraphic findings in progressive diaphyseal dysplasia.
A 14-yr-old white male with a severe form of progressive diaphyseal dysplasia (Engelmann-Camurati disease) was referred to our institution for evaluation of splenomegaly, which is not usually associated with the disease. Our studies included bone-marrow, and liver-spleen scans. These scintigraphic findings, along with the probable cause for splenomegaly, are discussed.
D000293:Adolescent; D001848:Bone Diseases, Developmental / Q000000981:diagnostic imaging*; D001853:Bone Marrow / Q000000981:diagnostic imaging*; D001842:Bone and Bones / Q000000981:diagnostic imaging; D003966:Camurati-Engelmann Syndrome / Q000150:complications / Q000000981:diagnostic imaging*; D004164:Diphosphonates; D006801:Humans; D008099:Liver / Q000000981:diagnostic imaging; D008297:Male; D011877:Radionuclide Imaging; D013154:Spleen / Q000000981:diagnostic imaging; D013163:Splenomegaly / Q000000981:diagnostic imaging* / Q000209:etiology; D013455:Sulfur; D013667:Technetium; D013669:Technetium Tc 99m Medronate; D013671:Technetium Tc 99m Sulfur Colloid
D004164:Diphosphonates; D013671:Technetium Tc 99m Sulfur Colloid; D013455:Sulfur; D013667:Technetium; D013669:Technetium Tc 99m Medronate