[Renal lesions in a case of tuberous sclerosis: association of angiomyolipoma, bilateral polycystic kidney and renal clear-cell carcinoma].
Association cases of tuberous sclerosis (ST) and renal displasia-tumors are infrequently seen in literature. These tumors are bilateral renal cystic displasia (RP) rare hamartomas, p.e. angiomyolipomas, and malignant neoplasms, p.e. renal clear cell carcinomas. There therefor as to the frequency of those pathological associations with ST, AML are frequently seen (50-80%). Reports of polycystic renal disease with ST are rare, whereas occasional associations of renal cell carcinomas with ST are founded out. By extensive literature examination of it's evident that the synchronous association of these pathological lesions is exceptional. This report describes one case of AML, RP and renal clear cell carcinoma in a female, 22 years old, with ST; the pathological, clinical and pathogenetic features are discussed.
D000230:Adenocarcinoma / Q000150:complications*; D000293:Adolescent; D000328:Adult; D001859:Bone Neoplasms / Q000556:secondary; D002648:Child; D002675:Child, Preschool; D005260:Female; D006391:Hemangioma / Q000150:complications*; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications*; D008067:Lipoma / Q000150:complications*; D008113:Liver Neoplasms / Q000556:secondary; D008175:Lung Neoplasms / Q000556:secondary; D007690:Polycystic Kidney Diseases / Q000150:complications*; D014402:Tuberous Sclerosis / Q000150:complications*
Lesioni renali in un caso di sclerosi tuberosa: associazione di angiomiolipoma, rene policistico bilaterale e carcinoma renale a cellule chiare.