[Cutis marmorata telangiectatica congenita. Apropos of a case with hemicorporeal topography. Ultrastructural study].
A case of hemicorporeal cutis marmorata telangiectatica congenita is described. The ultrastructural study showed dilated capillaries with an increase of pericytes number. Some particular elements are discussed: --rare occurrence of hemi-corporeal distribution; --ultrastructural aspects with increased pericytes, previously observed; --frequency of associated abnormalities, cutaneous hemangiomas, varix, difference of length of the limbs, ...; --more frequently regressive evolution; --etiopathogeny, still uncertain, with capillaries abnormalities, perhaps dysembryoplasic and/or induced by neurovegetative disorder. Teratogenic factors (drug, chemical or others) has been suggested but not proved.
D002196:Capillaries / Q000648:ultrastructure; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012867:Skin / Q000098:blood supply; D013577:Syndrome; D013684:Telangiectasis / Q000151:congenital* / Q000235:genetics / Q000473:pathology
Cutis marmorata telangiectatica congenita. A propos d'un cas de topographie hémicorporelle - Etude ultrastructurale.