[Fibrocystic disease of the pancreas: a presentation feature. Anatomopathological report].
Five patients with CF (cystic fibrosis) dead between 1974 to 1982 at ages ranging from one to six months are presented. All of them showed edema, hypoalbuminemia and anemia in a severely compromised clinical situation, and failure to gain weight in spite of being breast-fed in the first weeks of life, in four of them. All of them were second or third degree malnourished babies (Gomez classification) at admission. Five children presented edema, two severe, two moderate and one mild. Hematocrit values ranged from 19% to 39% (means 26.4%), and albuminemia from 1.60 to 3.00 g/% (means 2.14 g/%). Two patients presented antecedents of dead brothers. All of them received substitution therapy with pancreatic enzymes. The children dead within seven and seventeen days of admission (means ten days) of broncho-pulmonar disfunction. In this work, we wish to call the pediatrician's attention about the importance of making this diagnostic presumption in the first months of the life.
D001980:Bronchi / Q000473:pathology; D003550:Cystic Fibrosis / Q000473:pathology*; D004386:Duodenum / Q000473:pathology; D005260:Female; D005704:Gallbladder / Q000473:pathology; D006801:Humans; D007223:Infant; D008099:Liver / Q000473:pathology; D008297:Male; D010179:Pancreas / Q000473:pathology
Enfermedad fibroquística de páncreas: una forma de presentación. Descripción anatomopatológica.