[Chronic urticarial eruption with arthritis, papillary edema, and meningoencephalitis of childhood onset].
The authors report on a case of chronic urticarial eruption since infancy in a man who is now 27-year-old; the association of numerous chronic symptoms, principally meningo-encephalitis, polyarthritis, hepato-spleno-adenomegaly allows the authors to compare this case to those described by Prieur and Griscelli in 1981 and 16 others cases found in literature. It appears as a "systemic disease" without biological or immunological markers; it might belong to the group of chronic normocomplementemic vasculitis.
D000328:Adult; D001168:Arthritis / Q000150:complications*; D002648:Child; D002908:Chronic Disease; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D008590:Meningoencephalitis / Q000150:complications*; D008875:Middle Aged; D010211:Papilledema / Q000150:complications*; D013997:Time Factors; D014581:Urticaria / Q000150:complications*
Eruption urticarienne chronique avec arthrites, cedème papillaire, méningo-encéphalite à début infantile.