title: [Telangiectasias in progressive systemic sclerosis (generalized scleroderma). Observation on 120 cases].
abstract: 120 patients with progressive systemic sclerosis (PSS) were studied and subdivided into five groups according to the PSS classification of Giordano et al. ("acute diffuse scleroderma", "intermediate syndrome", "acrosclerosis sensu stricto", "sclerodactylia" and "sclerosis sine scleroderma"). In all five subgroups telangiectasias incidence was high (from 75% to 100%). The "ramosus" and "telangiectatic mats" types occur more frequently than other forms of telangiectasias. The former particularly involves the face, neck and chest; whereas the latter more usually involves the upper extremities and is the only type which appears at the lips. Cuticular telangiectasia is a third type, as important as the others but less frequent. The incidence of telangiectasias is related to disease duration. Similar telangiectasias have been observed in rarer patients with other connective tissue diseases (SLE, RA, dermatomyositis and undifferentiated connective tissue diseases).
mesh_terms: D001172:Arthritis, Rheumatoid / Q000175:diagnosis; D003240:Connective Tissue Diseases / Q000175:diagnosis; D003882:Dermatomyositis / Q000175:diagnosis; D003937:Diagnosis, Differential; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000175:diagnosis; D009260:Nail Diseases / Q000175:diagnosis; D012595:Scleroderma, Systemic / Q000175:diagnosis*; D013684:Telangiectasis / Q000175:diagnosis*
vernacular_title: Teleangiektasien bei der progredienten systemischen Sklerose (generalisierten Sklerodermie). Beobachtungen bei 120 Patienten.