Nonteratoid medulloepithelioma of the ciliary body.
A 34-month-old girl was treated for anterior uveitis, a superiorly subluxated cataract, rubeosis iridis and secondary glaucoma of the right eye of 3 months duration. She was diagnosed as having medulloepithelioma only after a mass was subsequently identified on the anterior surface of the iris. A low grade malignant nonteratoid medulloepithelioma was found to involve the ciliary surface throughout the circumference of the enucleated right globe. These tumors are generally associated with a good prognosis for survival, but are potentially lethal when they extend extrasclerally.
D002386:Cataract / Q000175:diagnosis; D002675:Child, Preschool; D002924:Ciliary Body / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D005901:Glaucoma / Q000175:diagnosis; D006801:Humans; D007499:Iris Diseases / Q000175:diagnosis; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000175:diagnosis* / Q000473:pathology; D014604:Uveal Neoplasms / Q000175:diagnosis* / Q000473:pathology; D014605:Uveitis / Q000175:diagnosis