Complex thoracic fistula in hereditary hemorrhagic telangiectasia.
Pulmonary arteriovenous fistula are not an uncommon finding in hereditary hemorrhagic telangiectasia; however, systemic pulmonary fistulas are exceptional. A case, characterized by its complex anatomical constitution, is described; the right suprascapular artery is the afferent systemic vessel and the efferent systemic and pulmonary drainage network sprung from a cirsoid aneurysmal tangle. The reasons for the development of the fistula are uncommon and probably multifactorial. Clinical diagnosis and management problems are discussed.
D000328:Adult; D000792:Angiography; D001164:Arteriovenous Fistula / Q000150:complications* / Q000000981:diagnostic imaging / Q000503:physiopathology; D005260:Female; D006439:Hemodynamics; D006801:Humans; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications*; D013909:Thorax