Idiopathic retroperitoneal fibrosis with diffuse involvement: further evidence of systemic idiopathic fibrosis.
We have presented a fatal case of idiopathic retroperitoneal fibrosis with an unusual diversity of systemic involvement, providing further evidence for the concept of systemic idiopathic fibrosis. Although the definitive cause of this disorder remains unknown, laboratory findings in this patient suggest an autoimmune process.
D000328:Adult; D001201:Ascites / Q000209:etiology; D003331:Coronary Vessels / Q000473:pathology; D005094:Exophthalmos / Q000209:etiology; D005260:Female; D006801:Humans; D012185:Retroperitoneal Fibrosis / Q000150:complications / Q000473:pathology*