[Extreme Ebstein's anomaly].
The incidence of Ebstein's anomaly among patients with congenital heart disease is about 0.5 and 1% among autopsy cases. Among 279 autopsy cases with congenital heart disease of the period from 1978 to 1982 we found 3 Ebstein's anomalies. The reported case is a rare combination of Ebstein's anomaly with ventricular L-loop, corrected transposition of the great arteries, atresia of aortic valve, hypoplasia of the aorta and of the aortic arch, coarctation of the aorta and septum secundum defect. Such a case has not been communicated in the literature. The case is described and the embryological development of the abnormalities is discussed.
D000015:Abnormalities, Multiple / Q000473:pathology*; D001017:Aortic Coarctation / Q000150:complications; D001021:Aortic Valve / Q000002:abnormalities; D004437:Ebstein Anomaly / Q000150:complications / Q000473:pathology*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D009206:Myocardium / Q000473:pathology; D014188:Transposition of Great Vessels / Q000150:complications
Extreme Ebstein-Anomalie.