[Case of XY-type gonadal dysgenesis with the development of bilateral gonadoblastomas].
We report a case of bilateral gonadoblastoma caused by xy-type true gonadal dysgenesis. Specific patterns in diagnostics and therapy are discussed. Due to rare entity interdisciplinary cooperation in management is emphasized.
D000328:Adult; D000568:Amenorrhea / Q000175:diagnosis / Q000473:pathology; D004407:Dysgerminoma / Q000175:diagnosis / Q000473:pathology*; D005260:Female; D006059:Gonadal Dysgenesis / Q000473:pathology*; D006061:Gonadal Dysgenesis, 46,XY / Q000175:diagnosis / Q000473:pathology*; D006801:Humans; D010051:Ovarian Neoplasms / Q000175:diagnosis / Q000473:pathology*
Ein Fall von reiner Gonadendysgensie des Typs XY mit Ausbildung doppelseitiger Gonadoblastome.