[Hepatic hemangiomatosis with congestive cardiac failure and development into a cholostatic hepatopathy].
The authors describe a case of hepatic hemangiomathosis in a three months old infant with a clinical picture of multiple cutaneous hemangioma, epatomegaly and severe cardiac failure. The cardiac catheterization with selective angiography showed extensive communication between the mammary artery and the hepatic circulation with the presence of large bloody areas into the markedly enlarged liver. The medical treatment with digitalis, diuretics, and corticosteroids obtained rapid resolution of the cardiac failure and of the A-V fistula signs. A clinical picture of severe liver cholostatic disease developed few months later which was confirmed by histological examination. The subsequent course has been favorable with complete clinical resolution of the liver disease.
D001649:Bile Duct Diseases / Q000209:etiology; D002675:Child, Preschool; D005260:Female; D006333:Heart Failure / Q000150:complications* / Q000188:drug therapy; D006391:Hemangioma / Q000150:complications*; D006529:Hepatomegaly / Q000150:complications; D006801:Humans; D008102:Liver Circulation; D008107:Liver Diseases / Q000209:etiology; D008113:Liver Neoplasms / Q000150:complications*; D008323:Mammary Arteries / Q000000981:diagnostic imaging; D011859:Radiography; D012878:Skin Neoplasms / Q000150:complications*
Emangiomatosi epatica con scompenso cardiaco congestizio ed evoluzione in epatopatia colostatica.