Cor pulmonale and facio-auriculo-vertebral sequence.
Two patients with facio-auriculo-vertebral sequence and cor pulmonale secondary to chronic airway obstruction responded rapidly and completely following surgical removal of normal-sized tonsillar and adenoidal tissue. Any child with a craniofacial malformation that includes diminished pharyngeal dimension or moderate micrognathia with midface hypoplasia must be observed closely, lest chronic progressive airflow impedance lead to right heart failure.
D000233:Adenoidectomy; D000402:Airway Obstruction / Q000150:complications*; D002574:Cervical Vertebrae / Q000002:abnormalities; D002675:Child, Preschool; D004423:Ear / Q000002:abnormalities; D005145:Face / Q000002:abnormalities*; D006801:Humans; D008297:Male; D011660:Pulmonary Heart Disease / Q000150:complications*; D014068:Tonsillectomy