[A variety of lymphomatoid granulomatosis, pseudosarcoid granulomatosis. An anatomo-clinical observation with an ultrastructural study].
A case of sarcoid-like granulomatosis involving the lung, skin and a large cervical vessel is presented. The patient died 4 years after the beginning of the disease with a diffuse angioimmunoblastic lymphadenopathy and a sarcomatous change. Although peculiar histological lesions were seen, with a majority of epithelioid and giant Langhans cells, the extra-pulmonary involvement and the poor prognosis were similar to those of the typical lymphomatoid granulomatosis (Liebow's disease).
D003937:Diagnosis, Differential; D006801:Humans; D008171:Lung Diseases / Q000473:pathology; D008230:Lymphomatoid Granulomatosis / Q000473:pathology* / Q000648:ultrastructure; D008297:Male; D008875:Middle Aged; D012507:Sarcoidosis / Q000473:pathology; D012871:Skin Diseases / Q000473:pathology
Une variété de granulomatose lymphomatoïde, la granulomatose pseudosarcoïdosique. Une observation anatomo-clinique avec étude ultrastructurale.