High excretion of beta-aminoisobutyric acid in patients with ketoacidosis.
High concentrations of beta-aminoisobutyric acid (BAIBA) were found to be present in the urine from patients with ketoacidosis. The R-form was always the dominating isomer of BAIBA. The finding is discussed, and it is suggested that the mechanism might be a derangement in the degradation of valine.
D000138:Acidosis / Q000652:urine*; D000596:Amino Acids / Q000032:analysis; D000621:Aminoisobutyric Acids / Q000652:urine*; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007536:Isomerism; D007662:Ketosis / Q000652:urine*; D008297:Male
D000596:Amino Acids; D000621:Aminoisobutyric Acids; C100049:2-aminoisobutyric acid