Vascular complications in the Ehlers-Danlos syndrome.
The Ehlers-Danlos syndrome is a rare condition, which usually is easily recognized. In one type of this disease, type IV, arterial fragility dominates, and the syndrome may remain undiscovered until the patient has a traumatic or spontaneous arterial rupture. Two cases with a fatal outcome are presented in order to emphasize some important aspects in the management of these patients.
D000328:Adult; D001158:Arteries / Q000293:injuries*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D006801:Humans; D008297:Male; D012422:Rupture, Spontaneous; D014652:Vascular Diseases / Q000209:etiology