Recurrent meningitis due to round-window fistula in Klippel-Feil syndrome. A case report.
Hearing is impaired in 30% of patients with Klippel-Feil syndrome, owing to a variety of anatomical deformities of the inner and middle ear cavities. Recurrent meningitis due to a stapedial footplate fistula associated with this syndrome is rare. A case of Klippel-Feil syndrome, deafness and recurrent meningitis due to a round-window fistula is described. Surgical sealing of the defect prevented further meningeal infections.
D003051:Cochlea / Q000002:abnormalities*; D005260:Female; D005402:Fistula / Q000150:complications*; D006319:Hearing Loss, Sensorineural / Q000150:complications; D006801:Humans; D007223:Infant; D007714:Klippel-Feil Syndrome / Q000150:complications*; D008583:Meningitis, Haemophilus / Q000209:etiology*; D008586:Meningitis, Pneumococcal / Q000209:etiology*; D012008:Recurrence; D012405:Round Window, Ear / Q000002:abnormalities*