Caroli's disease in childhood: report of two new cases.
Caroli's disease is a rare congenital disorder characterized by segmentary saccular dilatation of the intrahepatic bile ducts, which manifests itself clinically by cholangitis and bile stones. We report two cases of Caroli's disease in schoolgirls with clinical signs of recurrent abdominal pain associated with intermittent crises of cholestatic jaundice. Diagnosis was made by retrograde cholangiography in one patient and by intravenous cholangiography in the other.
D000005:Abdomen; D001649:Bile Duct Diseases / Q000151:congenital*; D001653:Bile Ducts, Intrahepatic; D002648:Child; D002761:Cholangitis / Q000209:etiology; D002769:Cholelithiasis / Q000209:etiology; D005260:Female; D006801:Humans; D008107:Liver Diseases / Q000151:congenital*; D010146:Pain; D012008:Recurrence