CT scan in a case of progressive generalized dystonia with amyotrophic paraplegia.
In a case characterized by progressive generalized dystonic paraplegia with amyotrophy and mental deficiency, CT scanning shows a bilateral lenticular nucleus hypodensity. A similar picture can be found in Wilson disease. However, this patient presented no biochemical, hepatic or ocular abnormalities.
D000328:Adult; D003342:Corpus Striatum / Q000000981:diagnostic imaging*; D003937:Diagnosis, Differential; D004421:Dystonia / Q000175:diagnosis / Q000000981:diagnostic imaging*; D006527:Hepatolenticular Degeneration / Q000175:diagnosis; D006801:Humans; D008297:Male; D010264:Paraplegia / Q000175:diagnosis / Q000000981:diagnostic imaging*; D013577:Syndrome; D014057:Tomography, X-Ray Computed