Alveolar soft part sarcoma of the tongue.
Alveolar soft part sarcoma is a rare malignancy. To our knowledge, 13 cases in the head and neck have been reported previously. It occurs more commonly in the extremities, where it is associated with a poor prognosis. Its clinical course resembles that of adenoid cystic adenocarcinoma in that late metastases often cause death in 10 to 15 years. A 5-year-old girl with alveolar soft part sarcoma was successfully treated with partial glossectomy and is free of disease at two-year follow-up.
D002675:Child, Preschool; D005260:Female; D005927:Glossectomy; D006801:Humans; D012509:Sarcoma / Q000473:pathology* / Q000601:surgery; D014059:Tongue / Q000473:pathology* / Q000601:surgery; D014062:Tongue Neoplasms / Q000473:pathology* / Q000601:surgery