Double zonal aganglionosis with a skipped oligoganglionic ascending colon.
We report a case of aganglionosis which involved the rectum, entire colon, appendix, terminal ileum but spared the ascending colon. This case was considered to represent for so-called double zonal aganglionosis. Histologically, the spared ascending colon proved to be an oligoganglionic segment. This may be the first documentation of a skipped oligoganglionic colon in double zonal aganglionosis.
D003106:Colon / Q000002:abnormalities* / Q000294:innervation / Q000473:pathology; D005724:Ganglia / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D007422:Intestines / Q000002:abnormalities / Q000294:innervation / Q000473:pathology; D008297:Male