Pulmonary capillary haemangiomatosis.
A Cypriot male of 22 years died after suffering recurrent daily haemoptyses of varying severity and slowly increasing effort intolerance for a period of four and a half years. Examination of a lung biopsy specimen revealed dilated vascular channels suggestive of a congenital anomaly of the pulmonary vasculature. Histological examination of the lung following necropsy revealed the diagnosis of pulmonary capillary haemangiomatosis. In this condition sheets of thin-walled blood vessels infiltrate the lung parenchyma, the walls of pulmonary arteries and veins, the bronchi and the pleura. The infiltration of pulmonary veins and venules induces secondary pulmonary veno-occlusive disease. This appears to be the second example of this disease which has been reported. It is open to clinical and histological mis-diagnosis and clinicians and pathologists should be aware of the existence of this entity.
D000328:Adult; D003535:Cyprus; D006391:Hemangioma / Q000473:pathology*; D006801:Humans; D008168:Lung / Q000098:blood supply; D008175:Lung Neoplasms / Q000473:pathology*; D008297:Male