Scoliosis and maple syrup urine disease.
The intermediate variant of maple syrup urine disease produced frequent infections and significant mental retardation in a young female patient recently treated for scoliosis. There were no problems with infection, wound healing, or fusion with a regimen consisting of a low protein diet, perioperative antibiotics, good hydration, and early postoperative ambulation.
D000293:Adolescent; D000900:Anti-Bacterial Agents / Q000627:therapeutic use; D005260:Female; D006801:Humans; D008375:Maple Syrup Urine Disease / Q000150:complications*; D011292:Premedication; D012600:Scoliosis / Q000150:complications* / Q000601:surgery; D013123:Spinal Fusion
D000900:Anti-Bacterial Agents