McCune-Albright syndrome (fibrous dysplasia) associated with an orbital tumor.
Craniofacial fibrous dysplasia has rarely been described in the polyostotic form of McCune-Albright disease. The unique ophthalmic features of interest in this patient with McCune-Albright's disease was the presence of an orbital tumor that suddenly increased in size compressing the optic nerve. Prompt excision of the tumor resulted in restoration to normal vision.
D002648:Child; D002675:Child, Preschool; D005094:Exophthalmos / Q000150:complications; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000150:complications*; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications* / Q000175:diagnosis; D006801:Humans; D007223:Infant; D009918:Orbital Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D012983:Soft Tissue Neoplasms / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography