title: Surgical repair of double-outlet right atrium.
abstract: The case of a patient with abnormal position of the atrial septum resulting in a right atrium with two atrioventricular valves and a disconnected left atrium is presented. The left superior vena cava drained into the left atrium; the right superior vena cava and the coronary sinus were absent. The surgical technique for repair of this anomaly is described. A possible explanation of the embryopathogenesis of double-outlet right atrium is given. To our knowledge, this is the second case of double-outlet right atrium to be reported in the thoracic surgical literature.
mesh_terms: D002315:Cardiopulmonary Bypass; D002648:Child; D006325:Heart Atria / Q000002:abnormalities; D006330:Heart Defects, Congenital / Q000196:embryology / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000601:surgery; D006801:Humans; D008297:Male; D011667:Pulmonary Veins / Q000601:surgery; D014683:Vena Cava, Superior / Q000002:abnormalities / Q000601:surgery