Double outlet left ventricle with intact ventricular septum.
Two cases of double outlet left ventricle with intact ventricular septum are reported. Both patients presented with neonatal cyanosis and signs of right ventricular outflow tract obstruction. Both have hypoplastic right ventricles with suprasystemic pressures, pulmonary to mitral valve continuity and the aorta in left-sided position. These seem to be the second and third cases of the malformation to be described thus far.
D000790:Angiocardiography; D001011:Aorta / Q000473:pathology; D004562:Electrocardiography; D006346:Heart Septum / Q000473:pathology; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000473:pathology; D014188:Transposition of Great Vessels / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery