title: [Adie's syndrome and polyneuropathy: apropos of a new case and a case of pupillotonia, polyneuropathy and generalized amyloidosis sparing the nerve].
abstract: The association of Adie's syndrome and of neuropathy of chronic evolution is not a frequent occurrence; first made known by Togi in 1967, four cases have been described ever since. The authors report two new observations: one concerns a man showing a unilateral tonic pupil associated to sensory neuropathy, raised C.S.F. protein, rarefaction of myelinated fibres with schwannian proliferation, without amyloid deposit. The other is that of a woman affected with bilateral pupillotonia, motor neuropathy of the four limbs and generalized amylosis. If the first observation is comparable to the five cases reported, the second is more questionable: the absence of amyloid deposit on three nerve biopsies and at the ciliary ganglion level does not absolutely exclude the possibility of amyloid neuropathy.
mesh_terms: D000270:Adie Syndrome / Q000175:diagnosis* / Q000473:pathology; D000368:Aged; D000686:Amyloidosis / Q000175:diagnosis* / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008297:Male; D009412:Nerve Fibers / Q000473:pathology; D009431:Neural Conduction; D011115:Polyneuropathies / Q000175:diagnosis* / Q000473:pathology; D011680:Pupil / Q000503:physiopathology
vernacular_title: Syndrome d'Adie et polyneuropathie: à propos d'un noveau cas et d'une observation de pupille tonique, polyneuropathie et amylose généralisée respectant le nerf.