Long-term follow-up in the unoperated univentricular heart.
Type A univentricular heart is a severe congenital cardiac defect; 50% of patients are dead 14 years after diagnosis, a death rate of 4.8% per year. Type C univentricular heart is even more lethal; 50% of patients are dead 4 years after diagnosis. Pulmonary stenosis did not protect either group of patients in terms of overall survival. Of the patients in class I or II at initial diagnosis, 34% of patients with type A and 12% of those with type C were in class III or IV or had died at follow-up. The most common causes of death were dysrhythmia, congestive heart failure and sudden and unexplained death.
D000368:Aged; D001145:Arrhythmias, Cardiac / Q000401:mortality; D003645:Death, Sudden / Q000209:etiology; D005260:Female; D005500:Follow-Up Studies; D006333:Heart Failure / Q000401:mortality; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D008297:Male; D009026:Mortality; D011666:Pulmonary Valve Stenosis / Q000401:mortality