title: Primary cholesteatoma in the congenitally atretic ear.
abstract: A developmental aberration significant enough to cause a congenital auricular atresia may well entrap ectodermal keratinous elements medial to an atresia plate, resulting in a primary cholesteatoma. We report such a case and discuss the proposed pathogenesis and pertinent embryology. A two-stage surgical procedure is offered as a reasonable management alternative when the cholesteatoma is well encapsulated.
mesh_terms: D000328:Adult; D002781:Cholesteatoma / Q000175:diagnosis* / Q000601:surgery; D004423:Ear / Q000002:abnormalities*; D006314:Hearing Loss, Conductive / Q000151:congenital; D006801:Humans; D008297:Male; D012086:Reoperation; D013701:Temporal Bone / Q000002:abnormalities