Sturge-Weber disease--neurophysiological evaluation of a case with secondary epileptogenesis, successfully treated with lobe-ectomy.
A case of Sturge-Weber's disease with a generalized seizure at 7 months of age is described, followed 7 months later by the development of very frequent and therapy resistent myoclonic astatic fits. The neurophysiological evaluation indicated a primary lesion in the right occipital area followed by signs of secondary epileptogenesis. The patient was cured by a right-sided occipital lobe-ectomy including an area of leptomeningeal angiomatosis.
D000798:Angiomatosis / Q000601:surgery*; D002540:Cerebral Cortex / Q000503:physiopathology; D004569:Electroencephalography; D004827:Epilepsy / Q000150:complications*; D005074:Evoked Potentials, Visual; D005260:Female; D006801:Humans; D007223:Infant; D009778:Occipital Lobe / Q000601:surgery*; D013341:Sturge-Weber Syndrome / Q000150:complications / Q000503:physiopathology / Q000601:surgery*