[Unusual recording of a giant pulmonary A wave on echocardiography in pulmonary atresia with an intact septum].
An infant with cyanotic congenital heart disease underwent M mode echocardiography, cardiac catheterisation and angiography. A diagnosis of pulmonary atresia with intact ventricular septum was made. Echocardiography showed an average sized right ventricle with tricuspid valve thickening, as previously described in this condition. In the pulmonary incidence, a giant A wave, occuring after the P wave of the surface ECG, without a systolic valvular opening, was recorded. This probably corresponded to the motion of the diaphragm separating the pulmonary infundibulum from the true pulmonary artery. The possibility of recording the giant A wave of the fibrous diaphragm should be recalled in patients with pulmonary atresia with intact ventricular septum.
D003964:Diaphragm / Q000503:physiopathology; D004452:Echocardiography; D004562:Electrocardiography; D006346:Heart Septum; D006801:Humans; D007231:Infant, Newborn; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000503:physiopathology
Enregistrement inhabituel d'une onde "A" géante pulmonaire en échographie (TM) lors d'une atrésie pulmonaire è septum intact.