Compressive myelopathy in Maroteaux-Lamy syndrome: clinical and pathological findings.
A 41-year-old woman with Maroteaux-Lamy syndrome developed spastic tetraparesis due to a compressive cervical myelopathy. There was substantial improvement following laminectomy and excision of the markedly thickened dura. Light and electron microscopic studies showed extensive accumulations of balloon cells in the dura.
D000328:Adult; D004388:Dura Mater / Q000473:pathology; D005260:Female; D006801:Humans; D009083:Mucopolysaccharidoses / Q000150:complications*; D009087:Mucopolysaccharidosis VI / Q000150:complications* / Q000473:pathology; D009128:Muscle Spasticity / Q000209:etiology; D009333:Neck; D011782:Quadriplegia / Q000209:etiology; D013117:Spinal Cord Compression / Q000209:etiology*