The ocular and periocular features of multicentric reticulohistiocytosis with paraproteinaemia. A report of two cases.
Two patients with atypical multicentric reticulohistiocytosis are reported. Skin rigidity with mobile rubbery nodules, and telangiectases, are typical of this disease and occurred around the eyes and elsewhere. One patient also had subconjunctival nodules and corneal crystal formation probably due to her paraproteinaemia. Some literature on this disease and on the occurrence of corneal crystal deposition in dysproteinaemia is reviewed.
D000368:Aged; D003315:Cornea / Q000473:pathology; D003460:Crystallization; D005123:Eye / Q000473:pathology*; D005143:Eyelids / Q000473:pathology*; D005145:Face / Q000473:pathology; D005260:Female; D006801:Humans; D008206:Lymphatic Diseases / Q000150:complications* / Q000473:pathology; D008854:Microscopy, Electron; D008875:Middle Aged; D010265:Paraproteinemias / Q000150:complications*; D012867:Skin / Q000473:pathology