[Interruption of the aortic arch and an aorto-pulmonary fistula. Simultaneous correction of lesions in a 5 1/2 month old infant].
Aortic arch hypoplasia is rare but carries a poor prognosis. It is usually associated with a left to right shunt at ventricular level. The association of an aorto-pulmonary fistula is exceptional. A case of a 5 1/2 month old infant treated successfully by simultaneous correction is reported with a review of the physiopathological changes. Pulmonary hypertension and aortic perfusion depend on the calibre of the ductus arteriosus and its evolution. The therapeutic problems which result are the suppression or palliation of pulmonary hypertension and resaturisation of distal aortic vascularisation. Surgery is the only hope of cure, and current techniques are reviewed: two stage procedures with revascularisation of the distal aorta and pulmonary artery banding, or simultaneous correction of aortic continuity with suppression of the left to right shunt under cardiopulmonary bypass. The technical conditions are analysed: perfusion of the different aortic segments, methods of reestablishing aortic continuity. Good results are as yet rare, and are obtained after complete correction under cardiopulmonary bypass.
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D001018:Aortic Diseases / Q000150:complications / Q000151:congenital* / Q000601:surgery; D005402:Fistula / Q000150:complications / Q000151:congenital* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D008722:Methods; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery
Interruption de l'arche aortique et fistule aorto-pulmonaire. Cure simultanée des lésions chez un enfant de 5 mois et demi.