[Heart with criss-cross ventricles associated with an obstruction of the ejection pathway of the left ventricle and a mitral anomaly].
A case of criss-cross heart with situs inversus associated with subvalvular aortic stenosis and mitral regurgitation in a 9 year old boy is reported. Surgical correction of the valvular abnormalities gave an excellent clinical and haemodynamic result. A review of the literature shows that this abnormality of rotation of the ventricles coexists with a concordant atrioventricular connection in 70 % cases; the ventriculoarterial connection is only discordant in 12 % cases. The right ventricle is always situated above the left ventricle. The most common associated lesions are usually accessible to surgery; ventricular septal defect (98 % cases); stenosis or atresia of the pulmonary artery (70% cases). However, right ventricular hypoplasia is also common (65 % cases). Six patients underwent surgical correction of the associated lesions with 4 successes and 2 deaths. Surgery is possible in these complex cardiac malformations with good results providing a precise preoperative anatomical diagnosis is made.
D001020:Aortic Stenosis, Subvalvular / Q000150:complications / Q000151:congenital* / Q000601:surgery; D002312:Cardiomyopathy, Hypertrophic / Q000151:congenital*; D002648:Child; D002675:Child, Preschool; D006345:Heart Septal Defects, Ventricular / Q000150:complications; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D008297:Male; D008944:Mitral Valve Insufficiency / Q000150:complications / Q000151:congenital* / Q000601:surgery; D011651:Pulmonary Artery / Q000002:abnormalities; D012857:Situs Inversus / Q000150:complications*
Coeur avec ventricules entrecroisés associé à une obstruction de la voie d'éjection du ventricule gauche et à une anomalie mitrale.