A further study of the bile acids in infants with coprostanic acidemia.
The structure of the bile acids in serum of infants with coprostanic acidemia was further investigated. The identity of 3 alpha-hydroxy-5 beta-cholestan-26-oic acid and 3 beta-hydroxy-5-cholesten-26-oic acid was confirmed. The biosynthesis of the 3 alpha, 7 alpha, 12 alpha-trihydroxy-5 beta-C29 dicarboxylic bile acid does not start from beta-sitosterol.
D000138:Acidosis / Q000097:blood*; D001647:Bile Acids and Salts / Q000097:blood*; D055598:Chemical Phenomena; D002621:Chemistry; D004083:Cholestanol / Q000378:metabolism*; D002777:Cholestanols / Q000096:biosynthesis / Q000097:blood; D002784:Cholesterol / Q000031:analogs & derivatives* / Q000097:blood; D006801:Humans; D007223:Infant; D009682:Magnetic Resonance Spectroscopy; D013058:Mass Spectrometry
C029437:3,7,12-trihydroxycholestan-26,29-dioic acid; C029436:3-hydroxycholestan-26-oic acid; D001647:Bile Acids and Salts; D002777:Cholestanols; C029435:3-hydroxy-5-cholestenoic acid; D004083:Cholestanol; D002784:Cholesterol