title: Structure, function and an inherited defect of 2-oxo acid dehydrogenase multienzyme complexes.
mesh_terms: D042942:3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); D000818:Animals; D006801:Humans; D007231:Infant, Newborn; D007658:Ketone Oxidoreductases / Q000172:deficiency / Q000378:metabolism*; D007700:Kinetics; D046911:Macromolecular Substances; D008297:Male; D008929:Mitochondria, Heart / Q000201:enzymology; D008970:Molecular Weight; D009097:Multienzyme Complexes / Q000172:deficiency / Q000378:metabolism*; D011768:Pyruvate Dehydrogenase Complex / Q000378:metabolism*; D015325:Pyruvate Dehydrogenase Complex Deficiency Disease; D013552:Swine
chemical_list: D046911:Macromolecular Substances; D009097:Multienzyme Complexes; D011768:Pyruvate Dehydrogenase Complex; D007658:Ketone Oxidoreductases; D042942:3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)