Enhanced proteolytic degradation of normal beta-galactosidase in the lysosomal storage disease with combined beta-galactosidase and neuraminidase deficiency.
D000818:Animals; D002417:Cattle; D004591:Electrophoresis, Polyacrylamide Gel; D004705:Endocytosis; D005347:Fibroblasts / Q000378:metabolism; D005677:G(M1) Ganglioside / Q000378:metabolism; D005696:Galactosidases / Q000378:metabolism*; D005733:Gangliosidoses / Q000201:enzymology*; D000882:Haplorhini; D006801:Humans; D008297:Male; D009439:Neuraminidase / Q000172:deficiency*; D013737:Testis / Q000201:enzymology; D013997:Time Factors; D001616:beta-Galactosidase / Q000378:metabolism*
D005677:G(M1) Ganglioside; D005696:Galactosidases; D009439:Neuraminidase; D001616:beta-Galactosidase