Properties of a protein activator of glycosphingolipid hydrolysis isolated from the liver of a patient with GM1 gangliosidosis, type 1.
D004789:Enzyme Activation / Q000187:drug effects; D005677:G(M1) Ganglioside / Q000378:metabolism; D005696:Galactosidases / Q000378:metabolism; D005698:Galactosylceramidase; D005733:Gangliosidoses / Q000378:metabolism*; D006023:Glycoproteins; D006028:Glycosphingolipids / Q000378:metabolism*; D006801:Humans; D006868:Hydrolysis; D066298:In Vitro Techniques; D008099:Liver / Q000378:metabolism*; D008970:Molecular Weight; D011506:Proteins / Q000302:isolation & purification* / Q000494:pharmacology; D049231:Saposins; D049128:Sphingolipid Activator Proteins
D006023:Glycoproteins; D006028:Glycosphingolipids; C483345:PSAP protein, human; D011506:Proteins; D049231:Saposins; D049128:Sphingolipid Activator Proteins; D005677:G(M1) Ganglioside; C018835:asialo GM1 ganglioside; D005696:Galactosidases; C021500:lactosylceramidase; D005698:Galactosylceramidase