Sleep abnormalities in four cases of dyssynergia cerebellaris myoclonica of Ramsay-Hunt.
The nocturnal sleep of four patients with dyssynergia cerebellaris myoclonica (DCM) of Ramsay-Hunt was recorded with a polygraph. The following features were observed: a reduction of spindles, K complexes and vertex spikes; frequent arousals; rare rapid eye movements with a modification of their morphology and pattern; change in sleep stage percentages. In addition, myoclonus and polyspike-and-wave complexes appeared less frequently during sleep than during wakefulness. Three generalized convulsive and sixteen clonic seizures were recorded during stage 3/4 or on arousal. The clinical and physiopathological implications of these data are discussed.
D000293:Adolescent; D002524:Cerebellar Ataxia / Q000175:diagnosis*; D002648:Child; D004569:Electroencephalography; D004831:Epilepsies, Myoclonic / Q000175:diagnosis; D004830:Epilepsy, Tonic-Clonic / Q000175:diagnosis; D005071:Evoked Potentials; D005260:Female; D006801:Humans; D008297:Male; D002527:Myoclonic Cerebellar Dyssynergia / Q000175:diagnosis* / Q000235:genetics; D012894:Sleep Stages; D012893:Sleep Wake Disorders / Q000175:diagnosis*