[Treatment of glycogenosis type III with total parenteral nutrition, continuous intragastric infusion and D-thyroxine].
A 4-year-old patient with glycogenosis type III suffered from hypoglycemic attacks during the night and from an enormous hepatomegaly. The latter was the cause of a life-threatening respiratory insufficiency. Shrinkage of the liver size was an urgent necessity. The beneficial influences of total parenteral nutrition, continuous intragastric infusion during the night, and of D-tyhroxin are described.
D001786:Blood Glucose / Q000378:metabolism; D002675:Child, Preschool; D003918:Dextrothyroxine / Q000627:therapeutic use*; D004750:Enteral Nutrition; D006008:Glycogen Storage Disease / Q000628:therapy*; D006010:Glycogen Storage Disease Type III / Q000628:therapy*; D006529:Hepatomegaly / Q000628:therapy; D006801:Humans; D007003:Hypoglycemia / Q000628:therapy; D008112:Liver Glycogen / Q000378:metabolism; D008297:Male; D010288:Parenteral Nutrition; D010289:Parenteral Nutrition, Total
D001786:Blood Glucose; D008112:Liver Glycogen; D003918:Dextrothyroxine
Die Behandlung der Glykogenose Typ III mit totaler parenteraler Ernährung, intragastraler Dauertropfinfusion und D-Thyroxin.