Morquio disease, type B: activation of GM1-beta-galactosidase by GM1-activator protein.
D002478:Cells, Cultured; D004789:Enzyme Activation; D005347:Fibroblasts / Q000201:enzymology; D005696:Galactosidases / Q000378:metabolism*; D005698:Galactosylceramidase; D006023:Glycoproteins; D006801:Humans; D007700:Kinetics; D009085:Mucopolysaccharidosis IV / Q000201:enzymology*; D011506:Proteins / Q000502:physiology*; D049231:Saposins; D012867:Skin / Q000201:enzymology*; D049128:Sphingolipid Activator Proteins
D006023:Glycoproteins; C483345:PSAP protein, human; D011506:Proteins; D049231:Saposins; D049128:Sphingolipid Activator Proteins; D005696:Galactosidases; C021500:lactosylceramidase; D005698:Galactosylceramidase