title: Buschke-ollendorff syndrome.
abstract: Buschke-Ollendorff syndrome or dermatofibrosis lenticularis disseminata with osteopoikilosis is a rare autosomal dominant condition characterized by focal sclerotic bone dysplasia and associated connective tissue nevi. The following case report not only illustrates classic findings in this disease but also demonstrates previously reported, but little known features.
mesh_terms: D000328:Adult; D005260:Female; D005350:Fibroma / Q000473:pathology*; D006801:Humans; D009506:Nevus / Q000150:complications / Q000473:pathology*; D010023:Osteopoikilosis / Q000150:complications / Q000473:pathology*; D010026:Osteosclerosis / Q000150:complications / Q000473:pathology*; D010437:Peptic Ulcer / Q000150:complications; D012878:Skin Neoplasms / Q000150:complications / Q000473:pathology*; D013577:Syndrome