[Hereditary pancreatitis. Two new kindreds ].
An acute pancreatitis was observed in 2 children belonging to two unrelated families in which a total of 8 kindreds also had pancreatitis. Evolution was so severe that it demanded parenteral feeding and partial pancreatectomy with Wirsung-intestinal shunting. The authors stress: the rarity of this condition (which has a dominant autosomal transmission), the lack of specificity, the severity in which pseudocysts predominate, the further occurrence of both diabetes and external pancreatic deficiency and finally, the risk of pancreatic carcinoma.
D000208:Acute Disease; D000328:Adult; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008297:Male; D010180:Pancreatectomy / Q000379:methods; D010195:Pancreatitis / Q000175:diagnosis / Q000235:genetics* / Q000628:therapy; D010288:Parenteral Nutrition; D010375:Pedigree
Pancréatite héréditaire. A propos de deux nouvelles familles.