Pulmonary hypertension. Its association with hepatic cirrhosis and iron accumulation.
A 62-year-old white woman was found to have pulmonary hypertension; a short time later hepatic insufficiency developed. At the time of autopsy, hepatic cirrhosis, "primary" pulmonary hypertension, and evidence of increased iron absorption and storage were found. Pulmonary hypertension is an unusual complication of portal hypertension that is being reported increasingly often.
D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications; D006976:Hypertension, Pulmonary / Q000150:complications* / Q000209:etiology / Q000473:pathology; D007501:Iron / Q000378:metabolism*; D008099:Liver / Q000378:metabolism; D008103:Liver Cirrhosis / Q000150:complications* / Q000378:metabolism / Q000473:pathology; D008875:Middle Aged
D007501:Iron