Lower esophageal rings as a cause of dysphagia in progressive systemic sclerosis--coincidence or consequence?
Lower esophageal rings were found in five of 40 consecutive patients seen with progressive systemic sclerosis. Three of these five patients had diffuse skin involvement and two had the CREST variant of progressive systemic sclerosis. All of the patients with lower esophageal rings had intermittent esophageal obstruction (initially attributed to esophageal dysmotility), but so did five of seven patients with esophageal strictures without lower esophageal rings. Esophageal bougienage relieved this symptom in four of the five patients with rings in which it was performed. Persistent relief of these obstructive symptoms (6-36 months) in the patients with rings was in contrast to the recurrent dilatations that have been needed in the group of patients with peptic strictures. In contrast to esophageal aperistalsis and/or stricture formation, the lower esophageal ring, perhaps as a consequence of chronic gastroesophageal reflux, may be a more treatable cause of dysphagia in patients with progressive systemic sclerosis.
D000328:Adult; D003680:Deglutition Disorders / Q000175:diagnosis / Q000209:etiology*; D004940:Esophageal Stenosis / Q000150:complications* / Q000175:diagnosis; D004943:Esophagogastric Junction / Q000002:abnormalities; D005260:Female; D006801:Humans; D011446:Prospective Studies; D012595:Scleroderma, Systemic / Q000150:complications*