Achalasia-like esophagus from amyloidosis. Successful treatment with pneumatic bag dilatation.
A 78-year-old man with amyloidosis involving the esophagus is described. The clinical and radiographic features resembled classic achalasia, while esophageal manometrics demonstrated aperistalsis, incomplete LES relaxation, but a normal LES resting pressure. A review of the literature suggests that esophageal amyloid may have variable presentations. This patient was successfully managed with forceful pneumatic bag dilatation.
D000368:Aged; D000686:Amyloidosis / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D004106:Dilatation; D004931:Esophageal Achalasia / Q000209:etiology*; D004935:Esophageal Diseases / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008297:Male