Clinical and dermatologic aspects of the hereditary intestinal polyposes.
Distinctive cutaneous lesions frequently accompany and occasionally precede the intestinal lesions in Gardner's syndrome, Peutz-Jeghers syndrome, and Muir's syndrome. Awareness of the dermatologic manifestations of these entities may facilitate early diagnosis in these potentially life-threatening hereditary disorders.
D000236:Adenoma / Q000473:pathology; D000328:Adult; D002648:Child; D002675:Child, Preschool; D004814:Epidermal Cyst / Q000473:pathology; D005736:Gardner Syndrome / Q000473:pathology; D006801:Humans; D007223:Infant; D007417:Intestinal Polyps / Q000235:genetics / Q000473:pathology*; D008297:Male; D010580:Peutz-Jeghers Syndrome / Q000473:pathology; D010859:Pigmentation Disorders / Q000473:pathology; D012871:Skin Diseases / Q000235:genetics / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology