[Intestinal lymphangiectasis: late complication of transportation of the great vessels corrected by the Mustard technic. A clinical case].
The Great Arteries Transposition corrected by Mustard's repair is often complicated with inferior vena cava obstruction with consequent intestinal lymphangiectasia and protein-losing enteropathy. We report a case of a 9 years old boy who underwent Mustard's repair and presented diarrhoea, abdominal pain, hypoproteinemia and ascites. The fecal elimination of 51Cr-labeled albumin was remarkable increased and the intestinal biopsy showed a noteworthy lymphangiectasia due to an hemodynamic overload. Therefore subjects with Great Arteries Transposition corrected by Mustard's repair should be valued in the post-surgical follow-up by 51Cr-labeled albumin fecal elimination and by intestinal biopsy, already sensitive in asymptomatic phase.
D002648:Child; D006801:Humans; D008201:Lymphangiectasis, Intestinal / Q000209:etiology* / Q000473:pathology; D008297:Male; D011183:Postoperative Complications; D011504:Protein-Losing Enteropathies / Q000209:etiology*; D014188:Transposition of Great Vessels / Q000601:surgery*
Linfangectasia intestinale: complicanza tardiva di una trasposizione dei grossi vasi arteriosi corretta con tecnica di Mustard. Caso clinico.