Persistent right sinus venosus valve.
A 13-year-old girl presented with clinical features of pulmonary stenosis and regurgitation. Haemodynamic studies suggested the presence of a right ventricular tumour. M-mode and two dimensional echocardiograms indicated one or probably two soft thin walled structures originating from the right atrium. At operation a persistent right sinus venosus valve was removed. One earlier case report described the M-mode echocardiographic features of this condition in a neonate who died shortly after operation. This report illustrates that a large persistent right sinus venosus valve may present clinically years after birth. Echocardiography played an important role in making the diagnosis.
D000293:Adolescent; D004452:Echocardiography; D005260:Female; D006351:Heart Valves / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D006439:Hemodynamics; D006801:Humans