[Myocardial fibrosis in cystic fibrosis. A new case report (author's transl)].
We report the case of a 9 month-old infant in whom acute heart failure was the presenting symptom of cystic fibrosis. Post-mortem examination showed lesions of myocardial fibrosis associated with typical lesions of cystic fibrosis in the pancreas. Hypoproteinemia and anemia were present and earlier could have suggested the correct diagnosis before the episode of acute heart failure. The analogy of the histologic myocardial changes in cystic fibrosis and in congenital lipomatosis of the pancreas suggests a common pathogeny related to the deficiency of the exocrine secretion of the pancreas.
D009202:Cardiomyopathies / Q000209:etiology*; D003550:Cystic Fibrosis / Q000150:complications* / Q000473:pathology; D006801:Humans; D007223:Infant; D008297:Male; D009206:Myocardium / Q000473:pathology; D010179:Pancreas / Q000473:pathology
Fibrose myocadique au cours de la mucoviscidose. A propos d'une nouvelle observation.