Unusual vascular ring in infant with pulmonary atresia and ventricular septal defect.
A 3-day-old infant investigated for cyanotic heart disease was found to have partial DiGeorge syndrome and pulmonary atresia with ventricular septal defect. The only source of pulmonary blood flow was a right-sided persistent ductus arteriosus which originated from an aberrant right subclavian artery. Such a vascular ring has not been described previously. Surgical treatment included a left-sided prosthetic shunt in infancy followed by resection of the ligamentum arteriosum and right subclavian artery during the second year of life.
D004062:DiGeorge Syndrome / Q000150:complications; D004374:Ductus Arteriosus, Patent / Q000150:complications; D006345:Heart Septal Defects, Ventricular / Q000150:complications*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities*; D013348:Subclavian Artery / Q000002:abnormalities* / Q000601:surgery