[Massive retroperitoneal haemorrhage in the Bourneville-Pringle syndrome (author's transl)].
Case-report of a 54 year-old patient who was admitted with the clinical picture of an acute abdomen on the basis of intraabdominal haemorrhage. X-ray investigation discounted the diagnosis of ruptured aortic aneurysm, the CAT scan showed a suspected acute haemorrhagic necrotising pancreatitis. At laparotomy, a fatty, bleeding kidney tumour was found growing into the retroperitoneal tissue. The histological frozen-section showed a leimyo liposarcoma of the kidney. Bourneville-Pringle's disease was only afterwards known to be the basic illness of the patient, as was verified at postmortem examination. From the knowledge of these new facts, both the CAT-scan and the intra-operative and histological findings could be correctly interpreted.
D000208:Acute Disease; D003937:Diagnosis, Differential; D006391:Hemangioma / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology; D006470:Hemorrhage / Q000209:etiology; D006801:Humans; D007680:Kidney Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology; D008067:Lipoma / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology; D008297:Male; D008875:Middle Aged; D010195:Pancreatitis / Q000175:diagnosis*; D011859:Radiography; D012187:Retroperitoneal Space; D014402:Tuberous Sclerosis / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging
Zur Differentialdiagnose der hämorrhagisch-nekrotisierenden Pankreatitis: Massive Einblutung in das Retroperitoneum bei Bourneville-Pringle-Syndrom.