[Double outlet chamber from the right ventricle with restrictive interventricular communication].
We report two cases with double outlet right ventricle and subaortic restrictive ventricular septal defect. Both had atrial situs solitus and atrioventricular concordance. There were no other associated defects. Both cases were diagnosed by means of an angiocardiographic study and case two was also studied anatomically. Additional data for the diagnosis were findings of left ventricular overload by the EKG; left atrial enlargement and signs of venocapillary hypertension by the chest X-rays; left ventricular/right ventricular pressure gradient by the hemodynamic study and the angiographic findings. One case had mitro-aortic discontinuity. Case two had a double infundibulum, being the left one the responsible for the restrictive ventricular septal defect. We conclude that double-outlet right ventricle with restrictive ventricular septal defect cases have their own clinical, hemodynamic and angiographic features which have to be accurately studied in order to offer an adequate surgical treatment.
D001013:Aorta, Thoracic / Q000002:abnormalities; D001021:Aortic Valve / Q000002:abnormalities; D002675:Child, Preschool; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging / Q000473:pathology*; D006345:Heart Septal Defects, Ventricular / Q000000981:diagnostic imaging / Q000473:pathology*; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D007223:Infant; D008297:Male; D008943:Mitral Valve / Q000002:abnormalities; D011859:Radiography
Doble cámara de salida de ventrículo derecho con comunicación interventricular restrictiva.