[Steidele complex (author's transl)].
Two new cases of type B congenital interruption of the aortic arch are described. Both had other congenital cardiovascular malformations as well as absence of the thymus and parathyroids. They were newborn male and female, their parents were young and healthy, admitted in our institution because of feeding difficulty, respiratory distress and cyanosis with signs of heart failure. Both were diagnosed at necropsy. According to the site of the interruption of the aortic arch, three types (A, B and C) of absence of the aortic arch are recognized. In our patients as in the majority of reported cases, the interruption of the aortic arch was associated with patent ductus arteriosus, ventricular septal defect and atrial septal defect, and other cardiovascular anomalies. The association of Di George syndrome with cardiovascular anomalies is commented.
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000473:pathology; D004062:DiGeorge Syndrome / Q000150:complications; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D010280:Parathyroid Glands / Q000002:abnormalities*; D013950:Thymus Gland / Q000002:abnormalities*
Complejo de Steidele.