[Pseudo-Hakim-Adams syndrome. Neuropsychological study of 23 cases of misdiagnosed Hakim-Adams syndrome].
The authors study the characteristics of a group of 23 patients for whom an initial tentative diagnosis of Hakim-Adams syndrome (H-A syndrome) was eventually rejected. On account of several factors distinguishing these patients from the true H-A group, the authors propose using the term "pseudo Hakim-Adams syndrome". The distinguishing factors include: the grounds for admission, i.e. mental or mnesic deterioration, associated with radiological images of ventricular dilatation; a clinical picture dominated by mental disorders with only rare disorders of gait and sphincter control (several neurological defects were direct consequences of previous cerebral disease); no antecedents of spontaneous meningeal hemorrhage or meningitis in the case history; neuropsychological examination showing fewer disorders of concentration and less dyscalculia and constructive dyspraxia than in true HA, and far more atypical signs of the aphasic and anxio-depressive type. The authors think that various pathological processes may be responsible for this pseudo H-A syndrome in which a predominant mental picture is associated with ventricular dilatation.
D000328:Adult; D000368:Aged; D003704:Dementia / Q000175:diagnosis*; D003951:Diagnostic Errors; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000175:diagnosis*; D006850:Hydrocephalus, Normal Pressure / Q000175:diagnosis*; D007427:Intracranial Pressure; D008297:Male; D001523:Mental Disorders / Q000175:diagnosis; D008875:Middle Aged; D009069:Movement Disorders / Q000175:diagnosis*; D011877:Radionuclide Imaging; D012711:Serum Albumin, Radio-Iodinated; D013346:Subarachnoid Space / Q000000981:diagnostic imaging; D013577:Syndrome; D014057:Tomography, X-Ray Computed
D012711:Serum Albumin, Radio-Iodinated
Pseudo-syndrome de Hakim et Adams. Etude neuropsychologique de 23 cas de faux diagnostic de syndrome de Hakim et Adams.