[Budd-Chiari syndrome with massive thrombosis of the subdiaphragmatic venous system and major fibrinopenia (author's transl)].
A 32-year-old patient without previous medical history died within three weeks of acute Budd-Chiari syndrome with massive thrombosis of the subdiaphragmatic venous system. No definite cause could be elicited. The course of the disease was complicated by anuria attributed to hepotorenal syndrome. Laboratory tests demonstrated major fibrinopenia. Detailed study of the haemostatic system was suggestive of hepatic failure associated with consumption coagulopathy of obscure origin.
D000328:Adult; D000347:Afibrinogenemia / Q000209:etiology*; D006502:Budd-Chiari Syndrome / Q000150:complications*; D003964:Diaphragm; D006801:Humans; D008297:Male; D013924:Thrombophlebitis / Q000209:etiology*; D013997:Time Factors
Syndrome de Budd-Chiari avec thrombose massive du système veineux sous-diaphragmatique et fibrinopénie majeure.