[Eosinophilic fasciitis (Shulman syndrome)].
Scleroderma like skin indurations without internal organ involvement, joint contractures, eosinophilia, and inflammatory infiltration of the fascia between subcutis and muscle are considered as characteristic features of eosinophilic fasciitis (EF). We report a further case of a 30 years old diabetic confirming to the syndrome defined by Shulman 1974. Corticosteroid therapy resulted in remission of disease symptoms, however a rebiopsy revealed no effect of therapy on histopathologic changes. A critical review of 118 cases in the literature is presented to explore the relationship of EF to scleroderma.
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D000328:Adult; D048909:Diabetes Complications; D003937:Diagnosis, Differential; D004802:Eosinophilia / Q000473:pathology*; D005208:Fasciitis / Q000150:complications / Q000175:diagnosis / Q000188:drug therapy / Q000473:pathology*; D006801:Humans; D008297:Male; D013577:Syndrome
D000305:Adrenal Cortex Hormones
Eosinophile Fasziitis (Shulman-Syndrom).