title: [Primary pulmonary hypertension in children].
abstract: Case report of an infant who, having been under cardiological observation since birth, developed the clinical symptoms of primary pulmonary hypertension at 12 months. The ECC showed right-ventricular hypertrophy, which progressed rapidly. Heart catheterization confirmed the suspected diagnosis of pulmonary hypertension without cardiovascular malformation. Treatment with isoproterenol and tolazoline was initiated but was unsuccessful: the child died at 18 months. The diagnosis was supported by the histopathology.
mesh_terms: D006328:Cardiac Catheterization; D004562:Electrocardiography; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D007223:Infant; D007545:Isoproterenol / Q000627:therapeutic use; D008297:Male; D011660:Pulmonary Heart Disease / Q000209:etiology* / Q000473:pathology; D014043:Tolazoline / Q000627:therapeutic use
chemical_list: D014043:Tolazoline; D007545:Isoproterenol
vernacular_title: Primäre pulmonale Hypertonie im Kindesalter.