Polysplenia syndrome: spectrum of gastrointestinal congenital anomalies.
This report describes four children with polysplenia syndrome seen in our hospital during the past year. Each had gastrointestinal abnormalities as their predominant problem, and two presented with gastrointestinal duplications not previously reported with this syndrome.
D000015:Abnormalities, Multiple / Q000601:surgery; D001652:Bile Ducts / Q000002:abnormalities; D002828:Choristoma; D004379:Duodenal Neoplasms / Q000473:pathology; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007422:Intestines / Q000002:abnormalities; D008099:Liver / Q000002:abnormalities; D008297:Male; D013154:Spleen / Q000002:abnormalities*; D013270:Stomach / Q000002:abnormalities