Intraorbital optic nerve hemangioblastoma with von Hippel-Lindau disease. Case report.
An intraorbital hemangioblastoma of the optic nerve is reported in a 23-year-old woman with von Hippel-Lindau disease. The absence of dural attachment and the microscopic findings were characteristic of hemangioblastoma. Four years later the patient developed a cystic hemangioblastoma in the left cerebellum which was successfully treated.
D000328:Adult; D000798:Angiomatosis / Q000150:complications*; D002528:Cerebellar Neoplasms / Q000150:complications / Q000473:pathology; D003390:Cranial Nerve Neoplasms / Q000150:complications* / Q000473:pathology; D005260:Female; D006394:Hemangiosarcoma / Q000150:complications* / Q000473:pathology; D006801:Humans; D009901:Optic Nerve Diseases / Q000150:complications* / Q000473:pathology; D009918:Orbital Neoplasms / Q000150:complications* / Q000473:pathology; D006623:von Hippel-Lindau Disease / Q000150:complications* / Q000473:pathology