[Acquired angioneurotic edema caused by acquired deficiency of C1 esterase inhibitor disclosing lymphoproliferative syndrome. Apropos of a case, review of the literature].
One case of acquired angio-neurotic oedema is described and discussed with the other cases recorded in literature since Caldwell's one in 1972. This entity is characterized by: --the late onset of angio-oedema but its presence only in about half cases, --a complement deficiency resulting from the lack of C1-esterase inhibitor, --the absence of familial identical cases, --the great frequency of associated illnesses overall lympho-proliferative diseases, --the therapeutic response to either etiologic treatment of the associated disease or to the symptomatic effect of drugs used in hereditary angio-neurotic oedema.
D000368:Aged; D000799:Angioedema / Q000209:etiology* / Q000276:immunology / Q000628:therapy; D003174:Complement C1 Inactivator Proteins / Q000097:blood / Q000172:deficiency*; D006801:Humans; D008232:Lymphoproliferative Disorders / Q000150:complications* / Q000276:immunology / Q000628:therapy; D008297:Male; D013997:Time Factors
D003174:Complement C1 Inactivator Proteins
Oedème angio-neurotique (acquis) par déficit acquis en inhibiteur de Ci-estérase révélateur d'un syndrome lympho-prolifératif. A propos d'un cas, revue de la littérature.