Myelokathexis: chronic neutropenia with hyperplastic bone marrow and hypersegmented neutrophils in two siblings.
The author describes the clinical and pathological characteristics of a chronic neutropenia in two siblings. The disease was probably inherited as an autosomal recessive trait. The clinical course and the results of the laboratory investigations corresponded to the rare cases of "myelokathexis" reported so far.
D000328:Adult; D000380:Agranulocytosis / Q000235:genetics*; D001853:Bone Marrow / Q000473:pathology; D002648:Child; D002908:Chronic Disease; D005260:Female; D006801:Humans; D009503:Neutropenia / Q000235:genetics* / Q000473:pathology; D009504:Neutrophils / Q000473:pathology