[Fanconi's disease associated with hepato-splenic peliosis (author's transl)].
The authors report a case of Fanconi's disease equilibrated for a period of 8 years by androgen therapy. The patient died after interruption of treatment; the clinical picture comprised hepatomegaly, jaundice, pancytopenia. The autopsy showed hepato-splenic peliosis and acute tuberculosis. The subject of peliosis is brought up to date by a thorough review of current literature and the relationships between steroid treatment and hepatic complications are discussed.
D000293:Adolescent; D000328:Adult; D000728:Androgens / Q000627:therapeutic use; D002648:Child; D002675:Child, Preschool; D005198:Fanconi Syndrome / Q000150:complications* / Q000188:drug therapy / Q000473:pathology; D005260:Female; D006801:Humans; D008099:Liver / Q000473:pathology; D008107:Liver Diseases / Q000150:complications*; D008297:Male; D010198:Pancytopenia / Q000150:complications; D010382:Peliosis Hepatis / Q000150:complications*
D000728:Androgens
Maladie de Fanconi avec péliose hépato-splénique.