Fibromatosis of dura presenting as infantile spasms.
A 6-month-old boy developed emprosthotonic infantile spasms and right hemiparesis. CT scan revealed a large mass related to a distended right temporal horn which on craniotomy proved to be a hard white tumour of the tentorium cerebelli which could be only incompletely resected. Microscopically and ultrastructurally, this lesion proved to be a typical fibromatosis containing myofibroblasts which invaded the brain. The child made an excellent recovery and is well a year after surgery. This case is another example which argues for full investigation of cases of infantile spasms which usually carry such a dismal prognosis.
D002528:Cerebellar Neoplasms / Q000175:diagnosis* / Q000473:pathology; D005350:Fibroma / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D008297:Male; D008854:Microscopy, Electron; D012640:Seizures / Q000209:etiology*