[Fever of undetermined origin in a case of total correction of persistent truncus arteriosus with agenesis of the left pulmonary artery (author's transl)].
A 19 month-old girl diagnosed of truncus arteriosus with absence of the left pulmonary artery and severe truncal valve insufficiency underwent total correction. A non previously diagnosed severe mitral insufficiency required a new operation to implant a Bjork-Shiley supraanular mitral prosthesis. The postoperative period was hemodynamically normal, except for the presence of persistent fever of unexplained origin. The clinical picture was thought to be an infectious endocarditis due to the late appearance of an aortic prosthetic leak. Because of failure to medical treatment a reoperation was performed to replace aortic prosthesis. Patient died eight hours postoperatively. Autopsy revealed a correct surgical repair, absence of endocarditis and severe miliary disseminated tuberculosis. Authors consider of interest to present this case-report due to the rarity of: a) correction of truncus with a single pulmonary artery under two years of age; b) associated mitral insufficiency; c) the presence of tuberculosis, difficult differential diagnosis with infectious endocarditis in a patient with valvular prosthesis.
D001021:Aortic Valve / Q000601:surgery; D005260:Female; D005335:Fever of Unknown Origin / Q000150:complications; D006350:Heart Valve Prosthesis; D006801:Humans; D007223:Infant; D008944:Mitral Valve Insufficiency / Q000150:complications / Q000601:surgery; D011651:Pulmonary Artery / Q000002:abnormalities*; D014339:Truncus Arteriosus, Persistent / Q000150:complications* / Q000601:surgery; D014391:Tuberculosis, Miliary / Q000150:complications
Fiebre de origen desconocido en un "truncus" con agenesia de la arteria pulmonar izquierda, intervenido de corrección total.