Esophageal web: a previously unrecognized complication of epidermolysis bullosa.
The course of the esophageal disease in four patients with epidermolysis bullosa dystrophica recessive is examined. Three of four patients experienced web formation, a previously unrecognized finding, and the significance of this lesion in the evaluation and management of these patients is emphasized. One of four patients underwent a successful colonic interposition for severe esophageal disease and the role of this potentially life-saving procedure is discussed.
D000293:Adolescent; D000328:Adult; D001464:Barium; D002648:Child; D002675:Child, Preschool; D003250:Constriction; D003680:Deglutition Disorders / Q000209:etiology; D003907:Dexamethasone / Q000627:therapeutic use; D004820:Epidermolysis Bullosa / Q000150:complications* / Q000188:drug therapy / Q000601:surgery; D004935:Esophageal Diseases / Q000188:drug therapy / Q000209:etiology* / Q000601:surgery; D004947:Esophagus / Q000000981:diagnostic imaging / Q000637:transplantation; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D011241:Prednisone / Q000627:therapeutic use; D011859:Radiography
D001464:Barium; D003907:Dexamethasone; D011241:Prednisone