Electrophysiologic findings in bilateral optic nerve hypoplasia.
Electrophysiologic studies were performed on 17 patients with bilateral optic nerve hypoplasia. Since most patients were infants, the diffuse light visual-evoked response was more helpful than the visual-evoked response obtained with pattern stimulation. In children over 1 year of age, the amplitude with diffuse light stimulation correlated well with other clinical measurements used to assess visual function. Before 6 months of age, it correlated better with visual prognosis than did clinical analysis. Photopic and scotopic electroretinographic measurements were normal in all except two in whom the scotopic b wave was supernormal.
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D004594:Electrophysiology; D004596:Electroretinography; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D009900:Optic Nerve / Q000503:physiopathology*; D009901:Optic Nerve Diseases / Q000503:physiopathology*; D010775:Photic Stimulation