Bleeding gastric telangiectasia. Complication of Raynaud's phenomenon, esophageal motor dysfunction, sclerodactyly and telangiectasia (REST) syndrome.
Anemia and skin telangiectasia were the main presenting features of a patient with Raynaud's phenomenon, esophageal motor dysfunction, sclerodactyly and telangiectasia (REST) syndrome. Diffuse gastric telangiectasia with chronic intermittent blood loss were responsible for the anemia. The multisystemic and progressive character of this collagenopathy in our patient is described and the endoscopic picture is presented. Management difficulties and treatment alternatives are discussed.
D000368:Aged; D001803:Blood Transfusion; D005260:Female; D005746:Gastric Emptying; D005764:Gastroesophageal Reflux / Q000150:complications; D005769:Gastrointestinal Motility; D005773:Gastroscopy; D006801:Humans; D007501:Iron / Q000627:therapeutic use; D011928:Raynaud Disease / Q000150:complications*; D012595:Scleroderma, Systemic / Q000150:complications; D013577:Syndrome; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications*
D007501:Iron