[Multifocal vitelliform dystrophy : a case report (author's transl)].
A case of multiple vitelliform dystrophy is described in an adult white woman ; vision, angiography, EOG are the same as in true Best's disease, but the reduction of vision seams more severe and occurs earlier. The extramacular discs are smaller, faster in evolution, they can appear, disappear or coalesce as in our case. The disease is genetically much less demonstrative than central vitelliform dystrophy. Angiographically, besides the usual pattern, they shaw marked staining without evidence of subretinal neovascularization perhaps due to a slight alteration of a still living RPE, and a hollow aspect of the discs at the level of RPE on stereo-angiograms. This is to be compared with the pathological findings made by Gass who described a marked thinning of the RPE.
D000328:Adult; D004585:Electrooculography; D005260:Female; D005451:Fluorescein Angiography; D006801:Humans; D008268:Macular Degeneration / Q000175:diagnosis* / Q000235:genetics; D014786:Vision Disorders / Q000175:diagnosis
Disques vitelliformes multiples. a propos d'un cas.