Testicular feminization syndrome (androgen insensitivity).
Three children with testicular feminization syndrome have been seen in the past 4 yr. Each presented with at least one large inguinal hernia. The gonad was proven to be a testis by frozen section. Gonadectomy and herniorrhaphy were done. The plan is to remove the second gonad after puberty. The causation and genetics of this condition are briefly discussed.
D013734:Androgen-Insensitivity Syndrome / Q000150:complications / Q000175:diagnosis* / Q000378:metabolism; D002648:Child; D005260:Female; D006552:Hernia, Inguinal / Q000150:complications; D006801:Humans; D007223:Infant; D008297:Male; D011944:Receptors, Androgen / Q000032:analysis*; D011987:Receptors, Steroid / Q000032:analysis*
D011944:Receptors, Androgen; D011987:Receptors, Steroid