Surgical treatment of the dilated aortic root in a child with Marfan's syndrome.
Life-threatening cardiovascular manifestations of Marfan's syndrome are rare in young children. The authors report the case of a 4 1/2-year-old girl with Marfan's syndrome who had a large aneurysm of the ascending aortic valve replaced and both coronary arteries implanted into a prosthetic graft (Bentall's procedure). Other published reports of children with aortic aneurysms due to Marfan's syndrome are reviewed.
D001014:Aortic Aneurysm / Q000209:etiology / Q000601:surgery*; D001021:Aortic Valve; D002675:Child, Preschool; D004108:Dilatation, Pathologic; D005260:Female; D006349:Heart Valve Diseases / Q000209:etiology / Q000601:surgery; D006350:Heart Valve Prosthesis; D006801:Humans; D008382:Marfan Syndrome / Q000150:complications*