"Inverse Chiari type II syndrome" in untreated hydrocephalus and its relationship to typical Arnold-Chiari syndrome.
Two cases of transtentorial upward displacement of the cerebellum in children with untreated hydrocephalus are reported. These cases clearly indicate that the condition is a primary malformation of the hindbrain and not a result of longstanding hydrocephalus treatment, as has been proposed in the past. The second case demonstrates the close relationship of the syndrome to classical Arnold-Chiari malformation.
D001139:Arnold-Chiari Malformation / Q000473:pathology*; D002531:Cerebellum / Q000002:abnormalities* / Q000473:pathology; D005260:Female; D006801:Humans; D006849:Hydrocephalus / Q000150:complications*; D007223:Infant