Pulmonary arterio-venous fistula in a child: a rare cause of congenital cyanosis.
A 12-year-old girl with a solitary pulmonary arterio-venous fistula (P.A.V.F.) affecting the R.L.L. is reported. The cyanosis was noted since birth and increased with age. The diagnosis was confirmed by right heart catheterization and pulmonary arteriography. Preoperatively, her hematocrit was 73%, paO2 36 mm Hg and no bruit was heard. The treatment consisted of a right lower lobectomy. One year postoperatively, the patient has normal activities, is asymptomatic and has no evidence of residual disease. A short review of the literature on the subject of P.A.V.F. is included and indicates the relative rarity of surgical treatment of this disease in childhood.
D001164:Arteriovenous Fistula / Q000150:complications / Q000601:surgery; D002648:Child; D003490:Cyanosis / Q000209:etiology*; D005260:Female; D006801:Humans; D011651:Pulmonary Artery / Q000000981:diagnostic imaging / Q000601:surgery; D011667:Pulmonary Veins / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography