Interrupted aortic arch type A associated with congenitally corrected transposition of great arteries and ventricular septal defect. Successful direct aortic anastomosis and pulmonary artery banding in an infant.
A case is described of congenitally corrected transposition of the great arteries (atrioventricular discordance, ventriculoarterial discordance) with interrupted aortic arch, a previously unreported association. Aortic continuity was achieved by direct surgical anastomosis. Pulmonary artery banding was subsequently necessary, because of heart failure associated with a large ventricular septal defect. A possible pathogenetic mechanism is suggested.
D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D004373:Ductus Arteriosus / Q000601:surgery; D006345:Heart Septal Defects, Ventricular / Q000150:complications* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000601:surgery; D014188:Transposition of Great Vessels / Q000150:complications*