Extramedullary plasmacytoma of the small intestine: first case report of ileocolic fistula and review of the literature.
Extramedullary plasmacytoma (EMP) of the small bowel is a rare entity previously reported as a cause of intestinal obstruction or bleeding. A case report of this disease entity presenting as an ileocolic fistula is reported. EMP is diagnosed by the following criteria: 1) absence of paraproteinemia; 2) absence of Bence Jones proteinuria; 3) normal skeletal survey; and 4) normal bone marrow biopsy specimen. Gastrointestinal plasmacytoma often occurs as a manifestation of multiple myeloma. EMP of the gastrointestinal tract is a rare manifestation of the disease, accounting for 13 per cent of all cases of EMP. It is a slow-spreading, radiosensitive tumor with a high tendency toward local recurrence. Surgical excision combined with radiotherapy is the treatment of choice for EMP of the gastrointestinal tract.
D006801:Humans; D007077:Ileal Diseases / Q000175:diagnosis / Q000209:etiology*; D007412:Intestinal Fistula / Q000175:diagnosis / Q000209:etiology*; D007414:Intestinal Neoplasms / Q000150:complications*; D008297:Male; D008875:Middle Aged; D010954:Plasmacytoma / Q000150:complications*; D012810:Sigmoid Diseases / Q000175:diagnosis / Q000209:etiology*