[A new case of epidermolysis bullosa dystrophica in a fifteen years old girl operated upon for pulmonary stenosis with a cardiopulmonary bypass (author's transl)].
The authors encountered technical difficulties for the endotracheal intubation but neither laryngeal damage nor serious oropharyngeal lesions occurred after this intubation. The general evolution was favourable without specific trouble (cutaneous or infectious). The risk of intubation was reexamined from the recent literature. It is generally believed that there is a tendency for the skin to become more resistant to the formation of bullae as the afflicted children grow older. So, when another disease sets vital prognosis in action, major surgical operations can be performed and more especially as the average length of life is now increasing for these patients.
D000293:Adolescent; D000758:Anesthesia; D002315:Cardiopulmonary Bypass; D004820:Epidermolysis Bullosa / Q000150:complications* / Q000151:congenital; D005260:Female; D006801:Humans; D007442:Intubation, Intratracheal; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000601:surgery*; D012151:Resuscitation
Epidermolyse bulleuse congénitale (dystrophique polydysplasique). Problèmes anesthésiques pour la chirurgie avec circulation extra-corporelle.