Pulmonary arteriovenous fistulas in association with hereditary hemorrhagic telangiectasia and carotid aneurysm.
A case is presented of a patient with multiple bilateral pulmonary arteriovenous fistulas, hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber Disease), and an intracranial carotid aneurysm. Over a twenty-five year period, the patient has survived several life-threatening complications, and has successfully undergone staged bilateral pulmonary lobectomies and clipping of the carotid aneurysm. Preoperative evaluation included cardiac catheterization studies both with and without temporary balloon occlusion of the pulmonary artery. The pathogenesis, clinical features, pathophysiologic changes, and treatment of pulmonary arteriovenous fistulas are discussed.
D000328:Adult; D000783:Aneurysm / Q000601:surgery*; D001165:Arteriovenous Malformations / Q000000981:diagnostic imaging / Q000601:surgery*; D002340:Carotid Artery Diseases / Q000000981:diagnostic imaging / Q000601:surgery*; D002343:Carotid Artery, Internal / Q000601:surgery; D005260:Female; D006801:Humans; D002538:Intracranial Arteriovenous Malformations / Q000000981:diagnostic imaging; D011013:Pneumonectomy; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011859:Radiography; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000601:surgery*