Plasmapheresis in hereditary angioneurotic edema and systemic lupus erythematosus.
A patient had hereditary angioneurotic edema coincident with systemic lupus erythematosus. This condition resulted in loss of hair, arthralgia, leukoplakia, collitis, and a nephrotic syndrome due to proliferative glomerulonephritis. The renal lesion was resistant to treatment with high-dose prednisolone and cyclophosphamide; however, sustained remission occurred after plasmapheresis. The patient has remained well for over two years since this procedure.
D000799:Angioedema / Q000150:complications / Q000235:genetics*; D003174:Complement C1 Inactivator Proteins / Q000172:deficiency; D005260:Female; D005921:Glomerulonephritis / Q000209:etiology / Q000628:therapy; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000150:complications*; D008875:Middle Aged; D010956:Plasmapheresis
D003174:Complement C1 Inactivator Proteins