Dejerine-Sottas disease revisited.
The fundamental clinical and pathologic findings associated with Dejerine-Sottas disease were reported in a series of three communications at the turn of the century. The salient pathologic observations made at that time regarding the characteristics of hypertrophic neuropathy occurring in infancy are recalled and reviewed in light of more recent studies.
D000293:Adolescent; D000328:Adult; D002420:Cauda Equina / Q000473:pathology; D002648:Child; D002675:Child, Preschool; D003711:Demyelinating Diseases / Q000473:pathology; D005260:Female; D006801:Humans; D006984:Hypertrophy; D007223:Infant; D008297:Male; D009133:Muscular Atrophy / Q000473:pathology; D009468:Neuromuscular Diseases / Q000175:diagnosis* / Q000235:genetics / Q000473:pathology; D010525:Peripheral Nerves / Q000473:pathology