Netherton's syndrome which responded to photochemotherapy.
We are reporting on a 22-year-old female patient with typical Netherton's syndrome who responded to photochemotherapy with the application of 8-MOP solution and irradiation with UVA. After two or three courses of PUVA therapy, each requiring 1 week, the skin condition improved. Maintenance photochemotherapy was necessary. Because there was a similarity between psoriasis and our case in the histological findings, this modality may be justified. No side effects were observed.
D000328:Adult; D005260:Female; D006201:Hair Diseases / Q000188:drug therapy* / Q000473:pathology; D006801:Humans; D007057:Ichthyosis / Q000188:drug therapy* / Q000473:pathology; D010778:Photochemotherapy; D011565:Psoriasis / Q000473:pathology; D013577:Syndrome; D014467:Ultraviolet Therapy