[Left diaphragmatic agenesis with digestive duplication and extra-lobar pulmonary sequestration (author's transl)].
The association of a diaphragmatic hernia and a pulmonary sequestration is known, though very rare. The authors present one singular observation because it were involved in aplasia of the homolateral pillar and a digestive duplication. They insist about the gravity of the reflux inherent to the malformation; they suggest its differed cure in spite of nutritional difficulties. Pathogenic considerations are advanced on that malformative complexe which is combined with the broncho-pulmonaries malformations of the foregut. It seems a direct proof of the theory of "the accessory lung". Finally, is underlined the gravity of the aplasia of the diaphragmatic leaf extensive to the pillar.
D000015:Abnormalities, Multiple / Q000473:pathology / Q000601:surgery*; D001998:Bronchopulmonary Sequestration / Q000150:complications* / Q000473:pathology / Q000601:surgery; D003964:Diaphragm / Q000002:abnormalities* / Q000601:surgery; D004065:Digestive System Abnormalities; D005764:Gastroesophageal Reflux / Q000601:surgery; D006548:Hernia, Diaphragmatic / Q000601:surgery; D065630:Hernias, Diaphragmatic, Congenital; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male
Agénésie diaphragmatique gauche avec duplication digestive et séquestration pulmonaire extra-lobaire.