2-hydroxy-2-methylsuccinic acid--a urinary metabolite in propionyl-CoA carboxylase deficiency.
D019735:Carbon-Carbon Ligases; D002648:Child; D005260:Female; D006801:Humans; D008025:Ligases / Q000172:deficiency* / Q000652:urine; D008293:Malates / Q000652:urine*
D008293:Malates; D008025:Ligases; D019735:Carbon-Carbon Ligases; C022458:propionyl CoA carboxylase (ATP-hydrolyzing); C011729:citramalate