The multiple nevoid basal cell carcinoma syndrome. Report of its occurrence in four generations of a family.
Four patients representing four generations of one family suffered from the multiple nevoid basal cell carcinoma syndrome. These cases are described and the importance of examination and careful supervision of the progeny of such patients is discussed. A unique finding in this series was a large congenital lung cyst occupying the left thoracic cavity of 1 patient.
D000293:Adolescent; D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000000981:diagnostic imaging / Q000235:genetics* / Q000473:pathology; D002280:Basal Cell Carcinoma / Q000235:genetics*; D002648:Child; D003560:Cysts / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008171:Lung Diseases / Q000000981:diagnostic imaging; D008175:Lung Neoplasms / Q000473:pathology; D008297:Male; D008339:Mandibular Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology; D008875:Middle Aged; D011859:Radiography; D012878:Skin Neoplasms / Q000473:pathology