Rapidly fatal lymphangioma-like Kaposi's sarcoma.
A 34-year-old black South African male was treated for lymphangioma-like clinical Kaposi's sarcoma. The disease followed a rapidly fatal course and was characterized by unexplained recurrent pleural effusions and severe refractory anaemia due to the presence of dilated vascular channels in the bone marrow. Definitive diagnosis was only made at autopsy. Lymphangiomatous changes in the skin without spindle cell formation caused diagnostic difficulties.
D000328:Adult; D003937:Diagnosis, Differential; D006801:Humans; D008200:Lymphangiectasis / Q000209:etiology; D008202:Lymphangioma / Q000473:pathology*; D008297:Male; D010996:Pleural Effusion / Q000209:etiology / Q000473:pathology; D012514:Sarcoma, Kaposi / Q000150:complications / Q000175:diagnosis / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology*