Acquired double-barrel oesophagus in epidermolysis bullosa dystrophica.
An unusual case of epidermolysis bullosa dystrophica with extensive stenosis, high perforation, and dissection of the oesophagus forming a "double-barrel" structure is described. Gastric epithelium found in the upper oesophagus is thought to be of metaplastic origin and caused by repeated minor trauma with repair.
D000328:Adult; D004820:Epidermolysis Bullosa / Q000150:complications* / Q000473:pathology; D004935:Esophageal Diseases / Q000209:etiology* / Q000473:pathology; D004947:Esophagus / Q000473:pathology; D005260:Female; D005753:Gastric Mucosa / Q000473:pathology; D006801:Humans