[Shulman's syndrome. A variant of scleroderma? Two cases (author's transl)].
Observations of two patients illustrating the problem of Shulman syndroma. The first had presented an oedema of the four limbs, without injury of the trunk, but with myalgias, histological fasciitis, eosinophilia and hypergammaglobulinemia. In spite of corticotherapy, evolution toward a generalized morphea. The second has presented the same oedema of the four limbs, with myalgias, but also Raynaud syndroma, histological fasciitis and eosinophilia. Evolution toward acrosclerosis in spite of corticotherapy. For the authors, Shulman's syndroma is apprehended as a particular clinical form of scleroderma.
D000368:Aged; D004487:Edema / Q000209:etiology; D004802:Eosinophilia / Q000473:pathology*; D005208:Fasciitis / Q000473:pathology*; D005260:Female; D006801:Humans; D012595:Scleroderma, Systemic / Q000473:pathology*; D012598:Sclerosis; D012867:Skin / Q000473:pathology; D013577:Syndrome
Syndrome de Shulman: une forme clinique des sclérodermie? A propos de deux cas.