[Cerebellar atrophy associated with lesions of the pallidum and luys' body and presence of lewy bodies. Relationships with degenerative disorders of the pallidum, substantia nigra and luys' body (author's transl)].
Clinical and pathological findings in a case of hereditary degenerative disease of the nervous system are reported. The clinical picture associated cerebellar signs with an action hypertonia, which was the cause of severe hypertonic paroxysms in the terminal stages of the illness. Pathological lesions were found in the cerebellar cortex, the external part of the pallidum, Luys' body, and the substantia nigra which included Lewy bodies. The relationships of this case with atrophic lesions of the pallidum and Luys' body are discussed.
D000368:Aged; D001284:Atrophy; D002526:Cerebellar Diseases / Q000473:pathology*; D005260:Female; D005917:Globus Pallidus / Q000473:pathology*; D006801:Humans; D008297:Male; D008875:Middle Aged; D009410:Nerve Degeneration; D009422:Nervous System Diseases / Q000473:pathology; D013378:Substantia Nigra / Q000473:pathology
Atrophie cérébelleuse et lésions pallido-luyso-nigriques avec corps de lewy. Rapports avec la dégénérescence pallido-luyso-nigrique.