title: [Hypertensive pulmonary vascular disease in children. Post-mortem study of 34 cases (author's transl)].
abstract: Report of a post-mortem study in 34 infants having presented pulmonary hypertension. Ages were between 16 days and three years old. One of the patients showed pulmonary lesion because of plexogenic arteriopathy of unknown etiology. The other 33 cases had congenital heart malformations. Macroscopic data as heart weight, thickness of the wall of the right ventricle and circumference of the pulmonary artery trunk were analized. Lesions developed in the pulmonary artery and its branches as well as those of the pulmonary veins are described. Different patterns of the hypertensive vascular disease are refered, emphasizing their evolution with the age of the patients. Some of the cases are particularly analized because of clinical, physiopathological or morphological peculiarities.
mesh_terms: D001344:Autopsy; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications / Q000473:pathology; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology / Q000473:pathology*; D007223:Infant; D007231:Infant, Newborn; D008168:Lung / Q000473:pathology; D008297:Male; D009206:Myocardium / Q000473:pathology; D011651:Pulmonary Artery / Q000473:pathology
vernacular_title: Enfermedad vascular pulmonar hipertensiva en niños. Estudio autópsico de 34 casos.