Congenital pulmonary valvular and infundibular stenosis complicating Ebstein's anomaly of the tricuspid valve. A case report.
Clinical, hemodynamic, angiographic, and echocardiographic as well as operative findings of a 19 years old girl are presented who had the unique combination of severe pulmonary valvular and infundibular stenosis with Ebstein's anomaly of the tricuspid valve. Pulmonary stenosis was relieved by infundibular resection and valvotomy. The atrial septal defect was closed with plication of atrialized ventricle and insertion of a porcine tricuspid prosthesis. Recatheterization 2 months postoperatively revealed disappearance of characteristic angiographic findings and slight residual gradient.
D000328:Adult; D000792:Angiography; D006328:Cardiac Catheterization; D004437:Ebstein Anomaly / Q000150:complications* / Q000175:diagnosis; D004452:Echocardiography; D005260:Female; D006801:Humans; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000151:congenital* / Q000175:diagnosis