Tricuspid atresia with double-outlet left atrium.
Clinical and pathologic findings of an unusual case of cardiac malformation are presented. The main features were those of atresia of the right atrioventricular valve associated with two distinct atrioventricular orifices connecting the morphologically left atrium to the underlying morphologically left ventricle. Other distinguishing characteristics were ostium secundum atrial septal defect, normally related great arteries, with the aorta arising from the main ventricular chamber and the pulmonary artery from the anterior and right-sided outlet chamber, and infundibular and valvular pulmonary atresia.
D000015:Abnormalities, Multiple / Q000473:pathology; D002648:Child; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000473:pathology; D006801:Humans; D008943:Mitral Valve / Q000002:abnormalities*; D014261:Tricuspid Valve / Q000002:abnormalities*