Management of infantile polyposis syndrome.
A boy with generalised infantile polyposis syndrome is reported to highlight the difficulties in management. Despite attempts to reduce polyp mass by regular endoscopic polypectomy, daily transfusions of blood products, and a trial of the non-steroidal anti-inflammatory agent sulindac, his condition gradually deteriorated and he died of septicaemia.
D000894:Anti-Inflammatory Agents, Non-Steroidal / Q000627:therapeutic use; D016913:Blood Component Transfusion; D003111:Colonic Polyps / Q000628:therapy*; D004724:Endoscopy; D017809:Fatal Outcome; D006801:Humans; D007223:Infant; D008297:Male; D018805:Sepsis / Q000209:etiology; D013467:Sulindac / Q000627:therapeutic use
D000894:Anti-Inflammatory Agents, Non-Steroidal; D013467:Sulindac