Mandibular resorption due to systemic sclerosis. Case report of surgical correction of a secondary open bite deformity.
Systemic sclerosis (SSc) is a connective-tissue disorder of unknown origin causing a multisystem disease. While erosions of the distal phalanges are commonly described, resorption of the mandible has been considered an unusual finding. However, systematic radiographic screening of different groups of patients suffering from SSc revealed a resorption incidence of 20-33% of the examined mandibles. Women especially seem to be affected, and the male/female ratio is 1/7. Bilateral condylysis due to SSc has been described in seven cases, or 13.7% of the reported cases. To the best of our knowledge, this is the fourth report of surgical correction of secondary dysgnathia due to systemic sclerosis and the first with a 2-year follow-up period.
D000328:Adult; D001862:Bone Resorption / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D016025:Bone Transplantation; D005260:Female; D005385:Fingers / Q000473:pathology; D006801:Humans; D015994:Incidence; D008310:Malocclusion / Q000209:etiology* / Q000601:surgery*; D008335:Mandibular Condyle / Q000000981:diagnostic imaging; D008336:Mandibular Diseases / Q000000981:diagnostic imaging / Q000209:etiology* / Q000601:surgery*; D011862:Radiography, Panoramic; D012008:Recurrence; D012595:Scleroderma, Systemic / Q000150:complications*