title: Orthognathic surgery in osteogenesis imperfecta: a case report with management considerations.
abstract: Osteogenesis imperfecta is a disease of connective tissues with additional metabolic defects. It is associated with recognisable facial disproportion and sometimes warrants surgical intervention for aesthetic, functional and psychological reasons. A severe case of osteogenesis imperfecta type 3 is presented to illustrate the feasibility of bimaxillary surgery using a mandibular body step osteotomy and maxillary down grafting at the Le Fort I level. The medical, anaesthetic, surgical and specific maxillofacial implications of surgery in these patients are discussed.
authors.affiliation: Department of Oral & Maxillofacial Surgery, University of Hong Kong.
authors.forename: I W
authors.initials: IW
authors.lastname: Ormiston
authors.forename: H
authors.initials: H
authors.lastname: Tideman
mesh_terms: D000328:Adult; D002508:Cephalometry; D017742:Dental Care for Chronically Ill; D003811:Dentinogenesis Imperfecta / Q000209:etiology; D005260:Female; D006801:Humans; D007569:Jaw Abnormalities / Q000209:etiology / Q000601:surgery*; D008334:Mandible / Q000601:surgery; D008437:Maxilla / Q000601:surgery; D010013:Osteogenesis Imperfecta / Q000150:complications*; D010027:Osteotomy / Q000379:methods