Orthognathic surgery in osteogenesis imperfecta: a case report with management considerations.
Osteogenesis imperfecta is a disease of connective tissues with additional metabolic defects. It is associated with recognisable facial disproportion and sometimes warrants surgical intervention for aesthetic, functional and psychological reasons. A severe case of osteogenesis imperfecta type 3 is presented to illustrate the feasibility of bimaxillary surgery using a mandibular body step osteotomy and maxillary down grafting at the Le Fort I level. The medical, anaesthetic, surgical and specific maxillofacial implications of surgery in these patients are discussed.
Ormiston
I W
IW
Department of Oral & Maxillofacial Surgery, University of Hong Kong.
Tideman
H
H
D000328:Adult; D002508:Cephalometry; D017742:Dental Care for Chronically Ill; D003811:Dentinogenesis Imperfecta / Q000209:etiology; D005260:Female; D006801:Humans; D007569:Jaw Abnormalities / Q000209:etiology / Q000601:surgery*; D008334:Mandible / Q000601:surgery; D008437:Maxilla / Q000601:surgery; D010013:Osteogenesis Imperfecta / Q000150:complications*; D010027:Osteotomy / Q000379:methods