XXXXY syndrome: report of case.
XXXXY Syndrome is a rare disorder characterized by multiple anomalies including growth deficiency, hypogenitalism, craniofacial anomalies and dental problems. Some experts feel this syndrome is a derivative of Klinefelter's Syndrome and may be associated with advanced maternal age. The case of a seven year old male with XXXXY syndrome is presented. A dental rehabilitation involving outpatient surgery is described.
Boraz
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Dental Service, University of Kansas Medical Center, Kansas City 66160-7334, USA.
D000015:Abnormalities, Multiple; D002547:Cerebral Palsy; D002648:Child; D003456:Cryptorchidism; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries; D002658:Developmental Disabilities; D005532:Foot Deformities, Congenital; D006228:Hand Deformities, Congenital; D006801:Humans; D007230:Infant, Low Birth Weight; D007231:Infant, Newborn; D008297:Male; D012729:Sex Chromosome Aberrations / Q000473:pathology*; D013577:Syndrome; D014960:X Chromosome