Surgical correction of pseudo-ainhum in Vohwinkel syndrome.
Vohwinkel syndrome or hereditary mutilating keratodermatitis is a rare condition producing palmoplantar hyperkeratosis and constricting rings of the fingers and toes which can progress to compromise neurovascular function and mobility. Medical treatment with oral retinol derivatives is recommended when its use is not contra-indicated. This paper describes surgical correction of the constricting rings on both hands in a 33-year-old woman affected by this condition.
Pisoh
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T
Department of Orthopaedics and Traumatology, Hopital Bichat, Paris, France.
Bhatia
A
A
Oberlin
C
C
D000328:Adult; D005260:Female; D005385:Fingers / Q000002:abnormalities / Q000601:surgery; D006228:Hand Deformities, Congenital / Q000235:genetics* / Q000601:surgery; D018737:Hand Strength / Q000502:physiology; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000235:genetics* / Q000601:surgery; D009048:Motor Skills / Q000502:physiology; D026741:Physical Therapy Modalities; D011182:Postoperative Care; D011183:Postoperative Complications / Q000503:physiopathology / Q000534:rehabilitation; D013524:Surgical Flaps / Q000379:methods; D016896:Treatment Outcome