title: [Agenesis of the right pulmonary artery with severe pulmonary hypertension, attenuated by surgical correction].
abstract: A 22 months old infant with agenesis of right pulmonary artery, without other associated congenital heart defects, is reported. Reconstruction of pulmonary arteries by connecting them through a 7mm Goretex tube was performed, with clear clinical improvement in view of disappearance of signs of cardiac insufficiency and of hypoxemia. Contralateral pulmonary hypertension, at systemic level, decreased to 77% in the immediate postoperative period. So, this technique becomes the first option, before considering these cases for cardiopulmonary transplantation.
authors.affiliation: Instituto do Coração do Hospital das Clínicas, FMUSP.
authors.forename: E
authors.initials: E
authors.lastname: Atik
authors.forename: M
authors.initials: M
authors.lastname: Barbero-Marcial
authors.forename: L
authors.initials: L
authors.lastname: Kajita
authors.forename: L N
authors.initials: LN
authors.lastname: Bustamante
authors.forename: A
authors.initials: A
authors.lastname: Foronda
authors.forename: M
authors.initials: M
authors.lastname: Ebaid
mesh_terms: D000792:Angiography; D002303:Cardiac Output, Low / Q000150:complications; D004562:Electrocardiography; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications / Q000601:surgery*; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery
vernacular_title: Agenesia da artéria pulmonar direita com acentuada hipertensão pulmonar, atenuada por correção cirúrgica.