Aortic calcification and renal cysts demonstrated by CT in a teenager with Alagille syndrome.
Alagille syndrome, or arteriohepatic dysplasia, is a disorder characterized by paucity of intrahepatic bile ducts, peculiar facies and skeletal anomalies. We report a typical case of this syndrome in an 18-year-old girl, in whom abdominal CT showed bilateral renal cysts and aortic wall calcification, findings unreported in the radiological literature.
Pombo
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F
Department of Radiology, Hospital Juan Canalejo, La Coruña, Spain.
Isla
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C
Gayol
A
A
Bargiela
A
A
D000293:Adolescent; D016738:Alagille Syndrome / Q000150:complications*; D001018:Aortic Diseases / Q000000981:diagnostic imaging*; D002114:Calcinosis / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D052177:Kidney Diseases, Cystic / Q000000981:diagnostic imaging*; D014057:Tomography, X-Ray Computed