[Diffuse cholangiocarcinoma in the context of multilobular liver cirrhosis as a manifestation of Wilson-Konovalov disease].
A 31-year-old female had a hepatolenticular degeneration. Multilobular cirrhosis and cholangiocellular liver carcinoma responsible for a rapid disease progression were found at necropsy. This is the first report of cholangiocarcinoma in Wilson-Konovalov disease.
Ponomarev
A B
AB
Kosminkova
E N
EN
Generalova
S Iu
SIu
D000328:Adult; D018281:Cholangiocarcinoma / Q000209:etiology*; D018450:Disease Progression; D005260:Female; D006527:Hepatolenticular Degeneration / Q000150:complications*; D006801:Humans; D008103:Liver Cirrhosis / Q000209:etiology*; D008113:Liver Neoplasms / Q000209:etiology*