[Congenital atrichia with cysts].
BACKGROUND
Congenital atrichia with papular lesions is a rare congenital ectodermic dysplasia.


METHODS
A male child had atrichia of the scalp and eyebrows from birth. The atrichia was associated with epidermic cystic lesions of the scalp. Biopsy showed cystic piler follicles within the derma surrounded with an inflammatory infiltration of multinucleated giant cells.


CONCLUSIONS
In most reported cases, scalp hair is present at birth and then falls within the first three months of life. Follicular cysts appear later. This syndrome generally occurs sporadically and the mode of inheritance is unknown.
Delprat
A
A
Service de Dermatologie, CHU Rangueil, Toulouse.
Bonafé
J L
JL
Lugardon
Y
Y
D000505:Alopecia / Q000151:congenital* / Q000473:pathology; D002675:Child, Preschool; D004814:Epidermal Cyst / Q000151:congenital*; D006197:Hair / Q000473:pathology; D006801:Humans; D008297:Male; D008859:Microscopy, Polarization; D012536:Scalp Dermatoses / Q000151:congenital*
Atrichie congénitale avec kystes.