Partial type of common atrioventricular canal defect associated with mitral stenosis.
We report a 63-year-old woman, with a partial type of common atrioventricular canal and mitral stenosis, who was hospitalized because of dyspnea on exertion. Two-dimensional echocardiogram showed an ostium primum atrial septal defect with two well-formed AV valves located at the same level. However, both anterior and posterior mitral leaflets were markedly thickened with a thickened subvalvular apparatus, and the commisures were fused. Echocardiographic measurements demonstrated a mitral valve area of 1.48 cm2 with mild mitral regurgitation. Cardiac catheterization demonstrated mild pulmonary artery hypertension with a large left to right shunt (72%) at the atrial level. The combination of the partial type of common atrioventricular canal and mitral stenosis is rare; only one similar case has been reported previously in the literature.
Moroi
M
M
Department of Internal Medicine, Toho University School of Medicine, Sakura Hospital, Chiba.
Ohsawa
H
H
Noike
H
H
Uchi
T
T
Okamoto
K
K
Kanai
M
M
Watanabe
E
E
Mineoka
K
K
Tomioka
H
H
Suzuki
M
M
D005260:Female; D006801:Humans; D008185:Lutembacher Syndrome / Q000175:diagnosis* / Q000503:physiopathology / Q000628:therapy; D008875:Middle Aged