[Erdheim's disease as a cause of sudden death].
Morphologic findings in three cases are presented. Death was caused by Erdheim's disease which was complicated by rupture of a false aneurysm of the ascending part of the aorta. A typical dystrophic involvement of the aortic wall at late stages of the disease is shown to be associated with a manifest inflammatory process presenting as nonspecific aortoarteritis. To verify the diagnosis, histologic examination of the aortic wall at some distance from the site of rupture should be performed.
Papkov
V G
VG
Tsyganov
K M
KM
Kordiukov
E V
EV
Averichev
A A
AA
D000328:Adult; D001011:Aorta / Q000473:pathology; D001019:Aortic Rupture / Q000473:pathology*; D001344:Autopsy; D003645:Death, Sudden / Q000209:etiology* / Q000473:pathology; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D009336:Necrosis; D013577:Syndrome
Bolezn' Erdgeĭma kak prichina vnezapnoĭ smerti.