[Cutaneous rhabdomyosarcoma].
OBJECTIVE
The occurrence of a rare alveolar rhabdomyosarcoma in a 16-year old girl seems worth of a case report.


METHODS
A large multinodular tumor developed on the buttocks and the external genitalia; systemic symptoms and metastases of lymph nodes and skin occurred very soon and the disease had a lethal outcome within 16 months. A temporary regression was observed after polychemotherapy with daunorubicine, vincritine and 5-fluoro-uracile.


CONCLUSIONS
In children the rhabdomyosarcoma is the most frequent sarcoma of soft tissues; the poor prognosis of the alveolar type is assessed by the case of this 16-year old girl; this tumor may progress as a systemic disease and present as a leukemia with rapid impairment of general health, enlargement of lymph nodes, cutaneous nodules and anemia.
Ndiaye
B
B
Clinique Dermatologique, CHU Le Dantec, Dakar, Sénégal.
Grosshans
E
E
Dieng
M T
MT
Kane
A
A
Develoux
M
M
Gentile
B
B
Jaubert
P
P
D000293:Adolescent; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D017809:Fatal Outcome; D005260:Female; D005833:Genital Neoplasms, Female / Q000473:pathology* / Q000628:therapy; D006801:Humans; D018232:Rhabdomyosarcoma, Alveolar / Q000473:pathology* / Q000628:therapy; D012878:Skin Neoplasms / Q000473:pathology* / Q000628:therapy; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000628:therapy
Rhabdomyosarcome cutané.