[Successful operation of a symptomatic aneurysm of the superior mesenteric artery in a child with Ehlers-Danlos syndrome].
Bleeding of an aneurysm--especially of a great vessel--represents a complication of Ehlers-Danlos syndrome that is often lethal. A successful operation of a symptomatic aneurysm of the superior mesenteric artery in a 12-year old girl with an Ehlers-Danlos syndrome type VI is reported. The aneurysm was resected and replaced by a venous graft. Four years postoperatively the artery is perfectly patent; a new aneurysm did not develop.
Peiper
M
M
Abteilung für Kinderchirurgie, Chirurgische Universitätsklinik Hamburg.
Kalmár
P
P
Kluth
D
D
Lambrecht
W
W
D000783:Aneurysm / Q000000981:diagnostic imaging / Q000601:surgery*; D015901:Angiography, Digital Subtraction; D002648:Child; D004535:Ehlers-Danlos Syndrome / Q000000981:diagnostic imaging / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D017538:Mesenteric Artery, Superior / Q000000981:diagnostic imaging / Q000601:surgery*; D011183:Postoperative Complications / Q000000981:diagnostic imaging; D014654:Vascular Patency / Q000502:physiology; D014680:Veins / Q000637:transplantation*
Erfolgreiche Operation eines symptomatischen Aneurysmas der Arteria mesenterica superior bei einem Kind mit Ehlers-Danlos-Syndrom.