title: [Melanotic neuroectodermal tumor in an infant].
abstract: BACKGROUND
  Melanotic neuroectodermal tumor is a mostly benign tumor, rare in childhood, essentially located in the head and neck region.
  
  
  METHODS
  A two-month-old girl was seen for a rapidly increasing odontogenic tumor which appeared cystic at the CT scan. After enucleation, this premaxillar tumor recurred one month later with an osteogenic aspect at the CT scan. Urine catecholamine excretion was normal; Methyl Iodo Benzyl Guanidin scintigraphy failed to show any fixation and electron microscopy examination of the biopsy showed several varieties of melanocytes. A partial maxillectomy was performed by oral approach. The patient is well 4 1/2 years later.
  
  
  CONCLUSIONS
  This observation confirms the recurrence potential of this tumor and the cosmetic interest of the oral surgical approach.
authors.affiliation: Clinique de stomatologie et de chirurgie maxillofaciale, CHU Timone, Marseille, France.
authors.forename: C
authors.initials: C
authors.lastname: Chossegros
authors.forename: F
authors.initials: F
authors.lastname: Cheynet
authors.forename: J C
authors.initials: JC
authors.lastname: Gentet
authors.forename: C
authors.initials: C
authors.lastname: Scheiner
mesh_terms: D005260:Female; D006801:Humans; D007223:Infant; D008441:Maxillary Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery; D017600:Neuroectodermal Tumor, Melanotic / Q000175:diagnosis / Q000473:pathology / Q000601:surgery
vernacular_title: Tumeur mélanotique neuroectodermique du jeune enfant.