title: Does hypoplasia of one pulmonary artery preclude a definitive repair in pulmonary atresia, intact ventricular septum, and hypoplastic right ventricle?
abstract: Twins with pulmonary atresia, intact ventricular septum, and hypoplastic right ventricle associated with underdeveloped and discontinuous left pulmonary artery are described. Operations to connect the left pulmonary artery to the main pulmonary trunk, with subsequent biventricular repair assisted by bidirectional cavopulmonary anastomosis and atrial fenestration were performed. Follow-up catheterization proved spontaneous closure of the fenestration in one patient. Both patients have been in a satisfactory condition for 3 years since operation.
authors.affiliation: Department of Pediatric Cardiology, Sakakibara Heart Institute, Tokyo, Japan.
authors.forename: K
authors.initials: K
authors.lastname: Suzuki
authors.forename: K
authors.initials: K
authors.lastname: Tatsuno
authors.forename: S
authors.initials: S
authors.lastname: Mimori
authors.forename: Y
authors.initials: Y
authors.lastname: Murakami
authors.forename: S
authors.initials: S
authors.lastname: Doi
authors.forename: Y
authors.initials: Y
authors.lastname: Takahashi
authors.forename: T
authors.initials: T
authors.lastname: Kikuchi
authors.forename: K
authors.initials: K
authors.lastname: Mori
mesh_terms: D000714:Anastomosis, Surgical; D002648:Child; D004200:Diseases in Twins; D005260:Female; D006346:Heart Septum; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D018633:Pulmonary Atresia / Q000601:surgery*; D014684:Venae Cavae / Q000601:surgery