Unexpected brainstem compression following routine surgery in a child with oto-palato-digital syndrome.
Oto-palato-digital syndrome type 1 is a rare condition with several features of concern to the anaesthetist. We report a patient who developed respiratory depression 5 h after general anaesthesia. This was subsequently found to be due to brainstem compression secondary to congenital deformities of the skull base and cervical vertebrae.
Clark
J R
JR
Department of Paediatric Intensive Care, Hospital for Sick Children, London.
Smith
L J
LJ
Kendall
B E
BE
Tasker
R C
RC
Wilkinson
K A
KA
D000293:Adolescent; D000768:Anesthesia, General; D001933:Brain Stem; D002574:Cervical Vertebrae / Q000002:abnormalities*; D002972:Cleft Palate / Q000601:surgery; D003251:Constriction, Pathologic / Q000150:complications; D006801:Humans; D008297:Male; D009958:Orofaciodigital Syndromes / Q000601:surgery*; D011183:Postoperative Complications; D012131:Respiratory Insufficiency / Q000209:etiology*; D012886:Skull / Q000002:abnormalities*; D013577:Syndrome