[Pulmonary atresia with intact ventricular septum. Natural development of the right ventricle].
A case of pulmonary atresia with intact ventricular septum and a hypoplastic right ventricle, with three wall formed portions, that became naturally well developed until 2 years of age, is related. A Blalock-Taussig shunt had been performed early in life. Z value of tricuspid valve of 0.3 and left ventricular in ECG has been changed to a well developed tricuspid annulus of 22 mm diameter and to a right ventricle overload after 2 years of follow-up, being possible surgical correction at that time. This observation, until today unknown, the natural increase of a congenitally hypoplastic cardiac chamber, favors the possibility to postpone the corrective operation to a better stage in this anomaly, when the risk becomes lower.
Atik
E
E
Instituto do Coração do Hospital das Clínicas-FMUSP.
Cury
A
A
Albuquerque
A M
AM
Ikari
N M
NM
Barbero-Marcial
M
M
Ebaid
M
M
D004452:Echocardiography; D004562:Electrocardiography; D005260:Female; D006352:Heart Ventricles; D006801:Humans; D007231:Infant, Newborn; D018633:Pulmonary Atresia / Q000175:diagnosis / Q000601:surgery*
Atresia pulmonar com septo interventricular integro. Desenvolvimento natural do ventrículo direito.