Small cell pleomorphic T-cell lymphoma presenting with cutaneous vasculitis.
The association between cutaneous vasculitis and lymphoproliferative disease has been increasingly recognized. We report a female patient who presented with cutaneous vasculitis which was due to a small cell pleomorphic T-cell lymphoma. In spite of aggressive therapy, she died two years after onset of disease. The clinical picture of vasculitis associated with lympho-proliferative disease is addressed with particular emphasis on symptoms and signs suggesting malignancy rather than vasculitis appearing in concert with well-defined connective tissue disorders.
Gran
J T
JT
Department of Rheumatology, Central Hospital of Aust Agder, Arendal.
Sund
S
S
Langholm
R
R
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D000328:Adult; D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D015451:Leukemia, Lymphocytic, Chronic, B-Cell / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology; D008228:Lymphoma, Non-Hodgkin / Q000175:diagnosis / Q000188:drug therapy / Q000503:physiopathology; D016399:Lymphoma, T-Cell / Q000175:diagnosis* / Q000188:drug therapy / Q000503:physiopathology; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000188:drug therapy / Q000503:physiopathology; D014657:Vasculitis / Q000209:etiology*
D000305:Adrenal Cortex Hormones