A unique left-to-right shunt characterized by multimodality cardiac imaging.
We describe the first reported patient with a persistent left superior vena cava that communicates directly with the left atrium as an isolated congenital defect. She developed mitral stenosis and physiologic conditions that favored left-to-right shunting--a modified Lutembacher's syndrome. Noninvasive cardiac imaging completely elucidated her cardiac anatomy and physiology.
Stein
J H
JH
Department of Medicine, Rush Medical College, Chicago, IL, USA.
Broderick
L
L
Neumann
A
A
Snell
R J
RJ
Hanashiro
P K
PK
Caralis
D G
DG
D017023:Coronary Angiography; D003326:Coronary Circulation; D017548:Echocardiography, Transesophageal; D005260:Female; D006801:Humans; D008185:Lutembacher Syndrome / Q000150:complications / Q000175:diagnosis*; D018810:Magnetic Resonance Angiography; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D008946:Mitral Valve Stenosis / Q000175:diagnosis / Q000209:etiology; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000000981:diagnostic imaging*