Gardner's syndrome.
Gardner's syndrome is an autosomal dominant genodermatosis. Familial polyposis of the colon, osteomas, and cutaneous epidermoid cysts are characteristic features. Colon cancer will develop in all affected individuals unless prophylactic colectomy is performed. The follow-up and management of patients with Gardner's syndrome require a coordinated effort by physicians with expertise in gastroenterology, general surgery, oral surgery, radiology, endocrinology, neurology, ophthalmology, and dermatology. Genetic and psychological counseling should also be available for these patients.
Perniciaro
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Department of Dermatology, Mayo Clinic, Jacksonville, Florida, USA.
D011125:Adenomatous Polyposis Coli / Q000473:pathology; D001859:Bone Neoplasms / Q000473:pathology; D003110:Colonic Neoplasms / Q000473:pathology*; D004814:Epidermal Cyst / Q000473:pathology; D005500:Follow-Up Studies; D005736:Gardner Syndrome / Q000235:genetics* / Q000473:pathology; D005817:Genetic Counseling; D006801:Humans; D010016:Osteoma / Q000473:pathology; D010348:Patient Care Team; D011230:Precancerous Conditions / Q000473:pathology*; D012871:Skin Diseases / Q000473:pathology