title: Systemic vasculitis complicating infantile autoimmune enteropathy.
abstract: An infant with unexplained sideroblastic anaemia and severe protracted diarrhoea due to autoimmune gut disease is reported. Despite treatment with an exclusion diet and immunosuppressive agents she developed a severe systemic vasculitic illness. Intensive treatment with plasmapheresis resulted in resolution of the vasculitic process but the child subsequently died after overwhelming septicaemia.
authors.affiliation: Department of Child Health, University of Wales College of Medicine, University Hospital of Wales, Heath Park, Cardiff CF4 4XW.
authors.forename: H R
authors.initials: HR
authors.lastname: Jenkins
authors.forename: F
authors.initials: F
authors.lastname: Jewkes
authors.forename: G M
authors.initials: GM
authors.lastname: Vujanic
mesh_terms: D000756:Anemia, Sideroblastic / Q000209:etiology; D001327:Autoimmune Diseases / Q000150:complications* / Q000628:therapy; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007166:Immunosuppressive Agents / Q000627:therapeutic use; D007223:Infant; D007410:Intestinal Diseases / Q000150:complications* / Q000628:therapy; D010956:Plasmapheresis; D018805:Sepsis / Q000209:etiology; D014657:Vasculitis / Q000209:etiology* / Q000628:therapy
chemical_list: D007166:Immunosuppressive Agents