title: [Medullary sponge kidney with severe renal function impairment: a case report].
abstract: The term medullary sponge kidney refers as a renal parenchymal malformation characterized by cystic dilatation of the collecting ducts. Although medullary sponge kidney is a congenital disease, it is rarely identified in childhood and is usually discovered in adulthood. We report a child with bilateral medullary sponge kidney who, in addition to typical urographic findings, presented an unfavorable evolution that ended in renal chronic insufficiency. This outlook is uncommon and is described in only 10% of affected subjects.
authors.affiliation: Divisione di Chirurgia Pediatrica, Ospedale Regionale di Vicenza, Italia.
authors.forename: C
authors.initials: C
authors.lastname: Pesce
authors.forename: B
authors.initials: B
authors.lastname: Colombo
authors.forename: E
authors.initials: E
authors.lastname: Nicolini
authors.forename: F
authors.initials: F
authors.lastname: Spata
authors.forename: F
authors.initials: F
authors.lastname: Cappellari
mesh_terms: D000293:Adolescent; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007676:Kidney Failure, Chronic / Q000175:diagnosis / Q000209:etiology*; D007677:Kidney Function Tests; D007679:Kidney Medulla; D007691:Medullary Sponge Kidney / Q000150:complications* / Q000000981:diagnostic imaging; D011859:Radiography; D013997:Time Factors; D014463:Ultrasonography
vernacular_title: Rene a spugna midollare con grave compromissione della funzionalità renale: descrizione di un caso.