Hemimegalencephaly, hemihypertrophy and vascular lesions.
We report on two children with hemihypertrophy and ipsilateral hemimegalencephaly. Vascular lesions in one were consistent with a diagnosis of the Klippel-Trénaunay-Weber Syndrome. MRI performed in the first days of life and at 1 month of age revealed the presence of the neuronal anomaly.


CONCLUSIONS
The occurrence of hemimegalencephaly in our patients indicates that hemihypertrophy and vascular dysplasia are pathogenetically related phenomena of a continuous spectrum in which this brain disorder may appear.
Cristaldi
A
A
Paediatric Division, S. Pertini Hospital, Roma, Italy.
Vigevano
F
F
Antoniazzi
G
G
di Capua
M
M
Andreuzzi
A
A
Morselli
G
G
Iorio
F
F
Fariello
G
G
Trasimeni
G
G
Gualdi
G F
GF
D001808:Blood Vessels / Q000002:abnormalities; D001921:Brain / Q000002:abnormalities*; D005260:Female; D006801:Humans; D006984:Hypertrophy; D007231:Infant, Newborn; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis*