[Congenital protein C deficiency with pulmonary infarction].
A 45-year-old man was admitted with left chest pain and hemoptysis. Chest CT on admission showed multiple areas of wedge-shaped consolidation in both lung fields. A perfusion lung scintigram showed bilateral deficits in both lungs, whereas a ventilation scintigram was normal. The serum concentration and the functional activity of protein C were 41% and 42%, respectively. The same results were obtained from studies of the patient's mother and two sons, which indicated that this was a case of congenital protein C deficiency with pulmonary infarction.
Myou
S
S
Division of Respiratory Medicine, Ishikawa Prefectural Central Hospital, Kanazawa, Japan.
Nishi
K
K
Saito
M
M
Ooka
T
T
Fujimura
M
M
Matsuda
T
T
D006801:Humans; D008297:Male; D008875:Middle Aged; D020151:Protein C Deficiency; D011655:Pulmonary Embolism / Q000209:etiology*