title: [Congenital protein C deficiency with pulmonary infarction].
abstract: A 45-year-old man was admitted with left chest pain and hemoptysis. Chest CT on admission showed multiple areas of wedge-shaped consolidation in both lung fields. A perfusion lung scintigram showed bilateral deficits in both lungs, whereas a ventilation scintigram was normal. The serum concentration and the functional activity of protein C were 41% and 42%, respectively. The same results were obtained from studies of the patient's mother and two sons, which indicated that this was a case of congenital protein C deficiency with pulmonary infarction.
authors.affiliation: Division of Respiratory Medicine, Ishikawa Prefectural Central Hospital, Kanazawa, Japan.
authors.forename: S
authors.initials: S
authors.lastname: Myou
authors.forename: K
authors.initials: K
authors.lastname: Nishi
authors.forename: M
authors.initials: M
authors.lastname: Saito
authors.forename: T
authors.initials: T
authors.lastname: Ooka
authors.forename: M
authors.initials: M
authors.lastname: Fujimura
authors.forename: T
authors.initials: T
authors.lastname: Matsuda
mesh_terms: D006801:Humans; D008297:Male; D008875:Middle Aged; D020151:Protein C Deficiency; D011655:Pulmonary Embolism / Q000209:etiology*