[The Gorlin-Goltz syndrome. A report of 2 cases].
Two cases of patients with Gorlin-Goltz syndrome are described. The Gorlin-Goltz syndrome is a polydistrectual, hereditary disease characterized by multiple keratocysts and basocellular nevomatosis. It is pointed out that the inconstancy of the main symptoms makes early diagnosis difficult. The histologic characteristics of odontogenic keratocysts and the possible etiopathogenetic relations between cystic lesions and hamartia of adjacent oral mucosa, as considered by Stoelinga, are also discussed. In view of the course of the cases presented, a surgical approach considering such potential findings, is supposed to favorably affect the clinical evolution in respect to a high relapsing drift.
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Servizio di Odontoiatria, Ospedale Civile P.F. Calvi, Noale, Venezia.
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D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D005260:Female; D006801:Humans; D008334:Mandible / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D008339:Mandibular Neoplasms / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D011862:Radiography, Panoramic; D014057:Tomography, X-Ray Computed
Sindrome di Gorlin-Goltz. Osservazione di due casi.