[Dominant heredity in tardive congenital glaucoma with high insertion of the iris].
Seven cases of tardive congenital glaucoma determined by a high insertion of the iris are analyzed. Biomicroscopy revealed in all cases irian stromal atrophy and the complete or incomplete, total or partial insertion of the iris at the level of trabeculum was gonioscopically observed. With respect to the reducing of trabecular space exposed to aqueous humour, tension increase appeared between 11 and 20 years old at three patients, between 21 and 30 years old at three patients and at 34 years old at one patient. The authors consider the age of 35 to be an age limit in tardive congenital glaucoma. The transmission was dominant with variable expressivity. The systematic examination of family members allowed the discovering of other cases of tardive congenital glaucoma, which were unknown or known as open-angle glaucoma cases. The associations between tardive congenital glaucoma and myopia delayed the setting of diagnosis which lead to a more serious evolution. In the therapy with myotics was not sufficient, protected filtering interventions and especially trepanotrabeculectomy were recommended.
Cernea
P
P
Clinique Ophtalmologique Craiova.
Preoteasa
D
D
D000293:Adolescent; D000328:Adult; D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D005260:Female; D005799:Genes, Dominant; D005901:Glaucoma / Q000151:congenital* / Q000175:diagnosis / Q000235:genetics* / Q000628:therapy; D006801:Humans; D007498:Iris / Q000002:abnormalities*; D008297:Male; D009216:Myopia / Q000175:diagnosis / Q000235:genetics; D010375:Pedigree
L'hérédité dominante dans le glaucome congénital tardif par haute insertion de l'iris.