Rare pulmonary manifestation of Ehlers-Danlos syndrome.
Ehlers-Danlos syndrome (EDS) is an inherited disorder of connective tissue with multiple thoracic manifestations. We present an unusual thoracic manifestation of EDS consisting of parenchymal cysts and fibrous and fibroosseous nodules. These manifestations may be related to an abnormal attempt at repair of parenchymal or vascular tears.
Murray
R A
RA
Department of Diagnostic Radiology, Cleveland Clinic Foundation, Ohio, USA.
Poulton
T B
TB
Saltarelli
M G
MG
Dweik
R A
RA
Litwin
D K
DK
Kirby
T J
TJ
Meziane
M A
MA
O'Donovan
P B
PB
D000293:Adolescent; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology; D005260:Female; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D008171:Lung Diseases / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology; D014057:Tomography, X-Ray Computed