[Congenital pulmonary lymphangiectasis].
Six rare cases of congenital pulmonary lymphangiectasis were presented. The macroscopic characteristic of the lungs was honeycomb appearance due to extreme dilatation of the lymphatic spaces in the subpleural, interlobular, peribronchial and perivascular connective tissue. They had thin walls lined by endothelium. The dilated lymphatics may be due to congenital developmental defects or obstruction of major lymphatics, but they appeared to be associated only with pulmonary venous hypertension.
Zhu
Q
Q
General Hospital of Nanjing Military Region.
Jin
C
C
Li
F
F
D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008171:Lung Diseases / Q000151:congenital* / Q000473:pathology; D008200:Lymphangiectasis / Q000151:congenital* / Q000473:pathology; D008297:Male