Atlantoaxial subluxation in children with seronegative enthesopathy and arthropathy syndrome: 2 case reports and a review of the literature.
We describe 2 HLA-B27 positive children with seronegative enthesopathy and arthropathy (SEA) syndrome who developed spontaneous (nontraumatic) atlantoaxial subluxation early in their disease course. Neither child had evidence of spinal cord compression but both had progressive atlantoaxial subluxation in spite of conservative treatment. Both underwent elective posterior cervical (C1-C2) fusion.
Foster
H E
HE
Department of Pediatrics, British Columbia's Children's Hospital, Canada.
Cairns
R A
RA
Burnell
R H
RH
Malleson
P N
PN
Roberton
D M
DM
Tredwell
S J
SJ
Petty
R E
RE
Cabral
D A
DA
D000293:Adolescent; D000937:Antigen-Antibody Reactions; D001268:Atlanto-Axial Joint; D002648:Child; D015796:HLA-B27 Antigen / Q000032:analysis; D006801:Humans; D007592:Joint Diseases / Q000150:complications*; D004204:Joint Dislocations / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000209:etiology*; D008279:Magnetic Resonance Imaging; D008297:Male; D011859:Radiography; D012216:Rheumatic Diseases / Q000150:complications* / Q000276:immunology; D013577:Syndrome
D015796:HLA-B27 Antigen