[Multiple entrapments neuropathy in adult polyglucosan body disease].
Adult polyglucosan body disease (APBD) is a rare condition characterized by neuropathy, dementia, upper motor neuron dysfunction and neurogenic bladder. For diagnosis, the presence of polyglucosan bodies (PB), or PAS (+) glucose polymers, must be demonstrated. In this description of a woman with APBD and multiple entrapment neuropathy, we discuss a possible role for morphological changes induced by PB in increasing susceptibility to pressure palsies.
Gil-Néciga
E
E
Unidad de Neurología, Complejo Hospitalario Llerena-Zafra, Badajoz.
Pareja
J A
JA
Chincón
I
I
Jarrín
S
S
Chaparro
P
P
D003711:Demyelinating Diseases / Q000150:complications; D005260:Female; D005936:Glucans / Q000032:analysis*; D006801:Humans; D008475:Median Nerve / Q000503:physiopathology*; D008875:Middle Aged; D009408:Nerve Compression Syndromes / Q000150:complications / Q000175:diagnosis* / Q000503:physiopathology; D009431:Neural Conduction; D010543:Peroneal Nerve / Q000503:physiopathology*; D011826:Radial Nerve / Q000503:physiopathology*; D013497:Sural Nerve / Q000737:chemistry / Q000503:physiopathology*; D013979:Tibial Nerve / Q000503:physiopathology*
D005936:Glucans
Neuropatía con atrapamientos múltiples en la enfermedad con cuerpos de poliglucosanos del adulto.