[Clinical and pathogenetic observation in a case of pulmonary hemosiderosis].
Pulmonary hemosiderosis is a rare disease of unknown aetiology, whose clinical, pathogenetic and prognostic aspects are still open to discussion. The authors report a case of pulmonary hemosiderosis in a 2 years and 3 months old girl. Peculiar features of this case include antibody deficiency (which may contribute to the pathogenesis of the disease) and severe and protracted melena. Fatal outcome, despite several therapeutic trials, confirms the poor prognosis of pulmonary hemosiderosis.
Cataldo
F
F
Clinica Pediatrica R, Presidio Ospedaliero Aiuto Materno, Palermo.
Varrica
D
D
Violante
M
M
Viani
G
G
Albeggiani
A
A
Ugazio
A G
AG
D000420:Albuterol / Q000627:therapeutic use; D000756:Anemia, Sideroblastic; D001991:Bronchitis / Q000503:physiopathology; D002675:Child, Preschool; D017809:Fatal Outcome; D005260:Female; D006486:Hemosiderosis / Q000188:drug therapy / Q000209:etiology / Q000503:physiopathology*; D006801:Humans; D007154:Immune System Diseases / Q000150:complications; D007074:Immunoglobulin G / Q000097:blood; D008168:Lung / Q000000981:diagnostic imaging / Q000503:physiopathology*; D011241:Prednisone / Q000627:therapeutic use; D011859:Radiography; D013431:Sulfates / Q000627:therapeutic use; D013601:T-Lymphocytes
D007074:Immunoglobulin G; D013431:Sulfates; D000420:Albuterol; D011241:Prednisone
Considerazioni clinico-patogenetiche su di un caso di emosiderosi polmonare.