[Multiple and recurrent paralysis of cranial nerves: primary Gougerot-Sjögren syndrome].
Over a period of 10 years, a 49-year-old man had 3 episodes of recurrent cranial nerve palsy regressing within a few weeks. Each episode was accompanied with acute inaugural headache and diplopia and once with sensory impairment of the trigeminal nerf and once with tinnitus. The diagnosis of Goujerot-Sjögren's syndrome was retained after demonstration of hypergammaglobulinaemia, a positive Rose Bengale test and histological examination of biopsy specimens from the accessory salivary glands which revealed advanced typical lesions. Clinically, impaired secretion was not obvious.
Bakouche
P
P
Service de Neurologie, Hôpital Tenon, Paris.
Ferroir
J P
JP
Guillard
A
A
D003389:Cranial Nerve Diseases / Q000209:etiology*; D004172:Diplopia / Q000209:etiology; D006261:Headache / Q000209:etiology; D006801:Humans; D008297:Male; D008875:Middle Aged; D010243:Paralysis / Q000209:etiology*; D012008:Recurrence; D012469:Salivary Glands / Q000473:pathology; D012859:Sjogren's Syndrome / Q000150:complications* / Q000473:pathology
Paralysies multiples et récidivantes des nerfs crâniens. Syndrome de Goujerot-Sjögren primitif.