[Nephrotic syndrome associated with symmetrical multiple lipomatosis (Madelung's disease)].
We present a case of multiple symmetric lipomatosis Type I (Madelung's disease) with severe organic affection, hepatic cirrhosis, sever sensitive polyneuropathy and neuropathic ulceration at the left lower limb. A nephrotic syndrome developed in a larval form due to proliferative glomerulonephritis as the result of a metainfectious complications of the infection at the lower limb. We discuss the etiopathogenicity of the organic affection and we highlight the pathogenic links between the disease and its complications.
Matamala Gimeno
C
C
Servicio de Medicina Interna B, Hospital Clínico Universitario, Zaragoza.
Pérez Calvo
J I
JI
Rodríguez Benavente
A M
AM
Moros
M
M
Pérez Villaroya
J C
JC
Bueno Gómez
J
J
D001706:Biopsy; D005921:Glomerulonephritis / Q000150:complications / Q000209:etiology / Q000473:pathology; D006801:Humans; D007668:Kidney / Q000473:pathology; D007871:Leg Ulcer / Q000150:complications; D008069:Lipomatosis, Multiple Symmetrical / Q000150:complications*; D008099:Liver / Q000473:pathology; D008103:Liver Cirrhosis / Q000150:complications / Q000473:pathology; D008297:Male; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000150:complications* / Q000473:pathology; D009422:Nervous System Diseases / Q000150:complications
Síndrome nefrótico asociado a la lipomatosis múltiple simétrica. Enfermedad de Madelung.