title: [Nephrotic syndrome associated with symmetrical multiple lipomatosis (Madelung's disease)].
abstract: We present a case of multiple symmetric lipomatosis Type I (Madelung's disease) with severe organic affection, hepatic cirrhosis, sever sensitive polyneuropathy and neuropathic ulceration at the left lower limb. A nephrotic syndrome developed in a larval form due to proliferative glomerulonephritis as the result of a metainfectious complications of the infection at the lower limb. We discuss the etiopathogenicity of the organic affection and we highlight the pathogenic links between the disease and its complications.
authors.affiliation: Servicio de Medicina Interna B, Hospital Clínico Universitario, Zaragoza.
authors.forename: C
authors.initials: C
authors.lastname: Matamala Gimeno
authors.forename: J I
authors.initials: JI
authors.lastname: Pérez Calvo
authors.forename: A M
authors.initials: AM
authors.lastname: Rodríguez Benavente
authors.forename: M
authors.initials: M
authors.lastname: Moros
authors.forename: J C
authors.initials: JC
authors.lastname: Pérez Villaroya
authors.forename: J
authors.initials: J
authors.lastname: Bueno Gómez
mesh_terms: D001706:Biopsy; D005921:Glomerulonephritis / Q000150:complications / Q000209:etiology / Q000473:pathology; D006801:Humans; D007668:Kidney / Q000473:pathology; D007871:Leg Ulcer / Q000150:complications; D008069:Lipomatosis, Multiple Symmetrical / Q000150:complications*; D008099:Liver / Q000473:pathology; D008103:Liver Cirrhosis / Q000150:complications / Q000473:pathology; D008297:Male; D008875:Middle Aged; D009404:Nephrotic Syndrome / Q000150:complications* / Q000473:pathology; D009422:Nervous System Diseases / Q000150:complications
vernacular_title: Síndrome nefrótico asociado a la lipomatosis múltiple simétrica. Enfermedad de Madelung.