West syndrome associated with porencephaly.
A 3-year-old boy with West syndrome who was shown to have a cystic lesion on magnetic resonance imagings underwent surgical treatment. He had been initially managed with several antiepileptic drugs, but abnormalities on electroencephalography (EEG) persisted. Histological examination of the cystic wall obtained during surgery suggested porencephaly. Two years and 2 months later the child remained seizure-free and his EEG remarkably improved.
Katano
H
H
Department of Neurosurgery, Nagoya City University Medical School, Japan.
Nagai
H
H
Aihara
N
N
Yamashita
N
N
Kamiya
K
K
Ishikawa
T
T
Kanayama
M
M
D000324:Adrenocorticotropic Hormone / Q000008:administration & dosage / Q000627:therapeutic use; D001927:Brain Diseases / Q000175:diagnosis / Q000453:epidemiology* / Q000601:surgery; D002675:Child, Preschool; D002998:Clonazepam / Q000008:administration & dosage / Q000627:therapeutic use; D015897:Comorbidity; D003560:Cysts / Q000175:diagnosis / Q000453:epidemiology* / Q000601:surgery; D004569:Electroencephalography; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D009567:Nitrazepam / Q000008:administration & dosage / Q000627:therapeutic use; D013036:Spasms, Infantile / Q000188:drug therapy / Q000453:epidemiology*; D016896:Treatment Outcome; D014635:Valproic Acid / Q000008:administration & dosage / Q000627:therapeutic use
D002998:Clonazepam; D014635:Valproic Acid; D000324:Adrenocorticotropic Hormone; D009567:Nitrazepam