Fourth ventricular hemangioblastoma associated with pheochromocytoma and renal medullary fibroma.
Intraventricular hemangioblastomas are exceptionally rare. Of the cases described in the literature, very few were associated with von Hippel-Lindau disease. We present a highly unusual case of a fourth ventricular hemangioblastoma associated with a pheochromocytoma and a renal medullary fibroma. This may represent a forme fruste of the von Hippel-Lindau complex. A workup for papilledema resulted in the discovery of this rare finding.
Ehrenpreis
S J
SJ
Friedenwald Eye Institute, Maryland General Hospital, Baltimore 21201.
Kristt
D A
DA
Rigamonti
D
D
D000310:Adrenal Gland Neoplasms; D000328:Adult; D002551:Cerebral Ventricle Neoplasms; D005350:Fibroma; D018325:Hemangioblastoma; D006801:Humans; D007679:Kidney Medulla; D007680:Kidney Neoplasms; D008297:Male; D009378:Neoplasms, Multiple Primary; D010673:Pheochromocytoma; D006623:von Hippel-Lindau Disease