Cranial reconstruction in osteogenesis imperfecta.
Although osteogenesis imperfecta (OI) is recognized as a cause of craniosynostosis, therapeutic endeavors have not been reported. We present an 8-month-old girl with type 3 OI, in whom bilateral occipital flattening, biparietal widening, and frontal narrowing were effectively managed with a combined surgical release and reconstruction and molding cap therapy. The quality of the calvarial bone in OI requires a modified approach to the conventional bone techniques commonly used in the correction of craniosynostosis deformities.
Eppley
B L
BL
Division of Plastic Surgery, James Whitcomb Riley Hospital for Children, Indiana University Medical Center, Indianapolis 46202.
Kalsbeck
J E
JE
Sadove
A M
AM
D003398:Craniosynostoses / Q000209:etiology / Q000601:surgery*; D003399:Craniotomy / Q000379:methods; D005260:Female; D006801:Humans; D007223:Infant; D010013:Osteogenesis Imperfecta / Q000150:complications* / Q000601:surgery