Polycystic kidneys associated with Marfan syndrome in an adult.
A 41-year-old man with Marfan syndrome was found to have polycystic renal disease and underwent emergency surgery for dissecting aneurysm of the ascending aorta. To our knowledge only two cases of this rare combination of hereditary disorders have been described in the literature.
Biermann
C W
CW
Department of Urology, University of Basel, Switzerland.
Rutishauser
G
G
D000328:Adult; D000784:Aortic Dissection / Q000150:complications / Q000601:surgery; D017544:Aortic Aneurysm, Abdominal / Q000150:complications / Q000601:surgery; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D007690:Polycystic Kidney Diseases / Q000150:complications*